İzole inferior vena cava kesintisinin prenatal tanısı ve klinik sonuçları: 12 vaka analizi

Yıl 2023, Cilt: 4 Sayı: 5, 530 - 534, 27.10.2023

Züat Acar , Işıl Turan Bakırcı , Deniz Kanber Acar , Helen Bornaun

https://doi.org/10.47582/jompac.1358089

Öz

Amaç: Bu çalışmanın amacı, izole inferior vena cava kesintisi (IIVC) vakalarını prenatal olarak tanılamak ve yönetmek için prenatal tanının önemini ve genellikle olumlu bir prognoza sahip olduğunu vurgulamaktı.

Yöntem: Bu çalışma, IIVC ile azygos devamı prenatal olarak tanı alan 12 fetusu içeren bir uzunlamasına çalışma tasarımını takip etti.. Ekokardiyografi ve sonografi değerlendirmeleri, fetal kalp görüntülemesi konusunda uzmanlaşmış perinatoloji ve kardiyoloji uzmanları tarafından gerçekleştirildi.

Bulgular: Bu çalışma, IIVC tanısı alan 12 fetusun prenatal olarak tanılandığını ve bu tanıların pediatrik kardiyologlar tarafından doğrulandığını gösterdi. Klinik sonuçlar genellikle olumlu oldu.

Sonuç: Bulgular, prenatal tanının IIVC vakalarını güvenilir bir şekilde tanılayabileceğini ve bu nadir vasküler anormalliğin genellikle olumlu bir prognoza sahip olduğunu vurguladı. Bu çalışma, IIVC'nin doğru bir şekilde yönetilmesinin önemini ve prenatal tanının yaşamın ileri dönemlerindeki klinik sonuçları etkileyebileceğini vurgulamaktadır.

Anahtar Kelimeler

Vena kava inferiorda izole kesinti, azigos devamı, prenatal tanı, ekokardiyografi.

Prenatal diagnosis and clinical outcomes of isolated interruption of the inferior vena cava: an analysis of 12 cases

Öz

Objectives: This study aimed to comprehensively investigate the clinical manifestations and outcomes of prenatally diagnosed isolated interrupted inferior vena cava (IIVC) with azygos continuation to shed light on the significance of prenatal diagnosis.

Methods: A longitudinal study involved 12 fetuses prenatally diagnosed with IIVC and azygos continuation. Detailed fetal anomaly scans and echocardiography were performed, and pediatric cardiologists confirmed postnatal diagnoses. Genetic testing and extensive follow-ups were also performed.

Results: The study confirmed the high diagnostic accuracy of prenatal identification, with 100% postnatal confirmation. Most patients exhibited favorable outcomes, emphasizing the importance of prenatal diagnosis. Genetic testing revealed normal chromosomal arrangements in all tested cases.

Conclusion: Our study underscores the vital role of prenatal diagnosis in managing isolated IIVC cases and highlights their generally favorable prognosis. This study contributes to understanding this rare vascular anomaly and its implications for clinical practice.

Anahtar Kelimeler

Isolated interruption inferior vena cava, azygos continuation, prenatal diagnosis, echocardiography.

Kaynakça

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