Aksiller Lenfadenopati: Tek Bir Lenfadenopati ile Kronik Granülomatöz Hastalık Tanısı Alan Çocuk Hasta

Yıl 2019, Cilt: 9 Sayı: 3, 217 - 220, 01.12.2019

Pınar Gür Çetinkaya Deniz Çağdaş Ayvaz İlhan Tezcan

Öz

Lenfadenit, kronik granülomatöz hastalığın (KGH) en belirgin bulgularından biridir. Katalaz pozi-tif mikroorganizmalarla tekrarlayan enfeksiyonlar, bu hastalarda mortalite ve morbiditeye neden olurlar. Hematopoetik kök hücre naklinden (HKHN) sonra pek çok komplikasyon görülmesine rağmen, KGH’deki tek kesin tedavi yöntemidir. Bu çalışmadaki olgumuz, persistan sol aksiller lenfadenopati ile başvurmuş olup bu sayede X’e bağlı KGH tanısı almıştır. Hastaya HLA tam uyumlu aile dışı vericiden başka bir merkezde HKHN yapıldı ve tam donör kimerizm sağlandı.

Anahtar Kelimeler

kronik granülomatöz hastalık; lenfadenopati; kök hücre nakli

Kaynakça

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