CLINICAL EXPERIENCES IN PRIMARY RETROPERITONEAL TUMORS

Öz

Objective: In this study, Selcuk University Faculty of Medicine between 2011 - 2013 follow-up at the Department of Pediatric Oncology and Pediatric Surgery clinic was operated by a total of 22 patients with retroperitoneal tumors were evaluated retrospectively .

Patients and Method: Retroperitoneal tumors were evaluated retrospectively during 2011-2013. The cases treated with primary retroperitoneal tumor, surgical treatment without other distant organ metastasis were included in the study. The files of the cases were primary diagnosis in terms of age, sex, tumor stage at the time of diagnosis, surgical treatment method, pathological diagnosis and follow-up reviewed retrospectively.

Results: 9 out of 22 cases (40%) male and 13 (60%) were female. Male mean age of 71 months ( 3-132 ) in the girls 37 months ( 6-204 ) . The histological results, 15 (68%) of neuroblastoma , 4 (18.5%) Wilms, 1 (4.5% ) Embryonal Rhabdomyosarcoma , 1 (4.5% ) Clear cell sarcoma , 1 (4.5% ) malignant nerve sheath tumors were evaluated . Eight of the cases (36%) were stage I, 7 (32%) were stage III, 7 (32%) stage IV.

Conclusion: In conclusion, 68% of our cases were neuroblastoma and 64% of the patients were stage III and stage IV at the time of diagnosis. Retroperitoneal tumors are generally diagnosed in advanced stages. We think that this is due to the anatomical localizations and the silent as far as the clinically advanced stage. 

Anahtar Kelimeler

• retroperitoneal tumor,neuroblastoma,pediatric

PRİMER RETROPERİTONEAL TÜMÖRLERDE KLİNİK DENEYİMLERİMİZ

Öz

Amaç: Bu çalışmada Selçuk Üniversitesi Tıp Fakültesi 2011-2013 tarihleri arasında Çocuk Onkoloji Anabilim Dalı’nda takipli ve Çocuk Cerrahisi Kliniğince opere edilen toplam 22 retroperitoneal tümörlü hastaların kayıtları retrospektif olarak değerlendirildi.

Olgular ve Yöntem: Retroperitoneal tümör nedeniyle 2011-2013 arasında cerrahi girişim yapılan olgular geriye dönük olarak incelendi. Primer retroperitoneal tümörü kontrol altına alınan, başka uzak organ metastazı olmayan cerrahi tedavi uygulanan olgular çalışmaya dahil edildi. Yaş, cinsiyet, primer tanı anında tümör evresi, cerrahi tedavi yöntemi, patolojik tanı ve takip açısından olguların dosyaları retrospektif olarak değerlendirildi.

Bulgular: Olgularımızın 9’u (%40) erkek, 13’ü (%60) kızdı.  Ortalama yaş erkeklerde 71 ay (3-132), kızlarda 37 ay (6-204) idi. Histopatolojik olarak olguların 15 (%68)’i nöroblastom,  4’ü (%18.5) wilms tümörü, 1’i (%4.5) embriyonal rabdomyosarkom, 1’i (%4.5) berrak hücreli sarkom, 1’i (%4.5) malign sinir kılıfı tümörü olarak değerlendirildi. Tanı anında olguların 8’i (%36) evre I, 7’si (%32) Evre III, 7’si (%32) evre IV safhasındaydı.

Sonuç: Olgularımızın %68’i nöroblastom olup, tanı anında hastaların %64’ü evre III ve evre IV idi. Anatomik lokalizasyonları nedeniyle ileri evrelere kadar sessiz tümörler olan retroperitoneal tümörlerin çoğu nöroblastomdur ve genellikle ileri evrelerde tanı alırlar. 

Anahtar Kelimeler

• retroperitoneal tümör,nöroblastoma,pediatrik

Kaynakça

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