Kore Benzeri Klinik Bulgular ve Epilepsinin Eşlik Ettiği Bilateral Striopallidodentat Kalsinosis: Olgu Sunumu

Yıl 2009, Cilt: 10 Sayı: 1, 13 - 16, 01.04.2009

Özge Yılmaz-küsbeci Mehmet Yaman Alpay Haktanır Aylin Yücel

Öz

Bilateral striatopallidodentat kalsinozisle (BSPDK) nadir görülen, çeşitli semptomların bir arada görülebildiği ve bazal ganglionlar, serebellum ve serebral beyaz cevherde kalsiyum ve diğer minerallerin birikmesi ile karakterize bir hastalıktır. Genellikle idyopatik olarak görülmekle birlikte hipoparatiroidizm ve hipokalsemi birlikteliği, en sık görülen sekonder BSPDK nedenidir. Bu çalışmada hipoparatiroidizme bağlı olarak BSPDK saptanan ve hipokalsemi tablosunun düzeltilmesi ile klinik olarak belirgin iyileşme gösteren bir vaka sunulacaktır

Anahtar Kelimeler

Striopallidodental kalsinosis, hipokalsemi, hipoparatiroidizm

Kore Benzeri Klinik Bulgular ve Epilepsinin Eşlik Ettiği Bilateral Striopallidodentat Kalsinosis: Olgu Sunumu

Öz

Anahtar Kelimeler

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Kaynakça

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