Nadir Karşılaşılan Sık Karıştırılan Bir Tümör: Lenfanjiyoma Sirkumskriptum (Yüzeyel Lenfatik Malformasyon)

Yıl 2019, Cilt: 14 Sayı: 3, 145 - 147, 15.11.2019

Alper Ural Fatma Bilgen Abdülkadir Yasir Bahar Mehmet Bekerecioğlu

https://doi.org/10.17517/ksutfd.455818

Öz

Lenfanjiyoma Sirkumskriptum yüzeyel lokalize bir lenfanjiom varyantıdır.
Karakteristik klinik prezentasyonu kümelenmiş vezikül yada papüloveziküller
şeklindedir. Çoğu lenfanjiyomlar konjenital gelişmesine rağmen erişkin yaşlarda
da görülebilmektedir.Bu yazıda kliniğimizde tedavi ettiğimiz sağ aksiller
bölgede ve meme başında nüks etmiş bir lenfanjioma sirkumskriptum olgusu
sunulmuştur. Lenfanjiyoma
sirkumskriptum hastalığının tekrarlama ve ikincil malignite gelişebilmesi
nedeniyle doğru tanı ve tedavi çok önemlidir. Çeşitli tedavi seçenekleri
olmasına karşın özellikle rekürren vakalar için cerrahi eksizyon altın standart
olup hastaların takibe alınması elzemdir.

Anahtar Kelimeler

lenfanjioma sirkumskriptum, vasküler tümörler, yüzeyel lenfatik malformasyon

A Rarely Encountered, Frequently Misleading Tumor: Lymphangioma Cirkumscriptum (Superficial Lymphatic Malformation)

Öz

Lymphangioma Circumscriptum is a superficially localized variant of
lymphangioma. The characteristic clinical presentation is a grouping of
vesicles or papulovesicles. Though most lymphangiomas develop congenitally, the
lymphangioma circumscriptum subtype is known to present also in adults.We
report a case of recurrent lymphangioma circumscriptum on the right axillary
and periareolar area treated in our clinics. Accurate diagnosis and treatment is crucial in cases of lymphangioma
circumscriptive  because of the
possibility of recurrence of this disease and the possibility of developing
malignancy secondarily. Besides the various treatment modalities, surgical excision is the gold
standard especially for recurrent cases and the patients need to be
followed-up.

Anahtar Kelimeler

circumscriptum, lymphatic malformation, vascular tumors

Kaynakça

• Referans 1- A. Alqahtani, L. T. Nguyen, H. Flageole, K. Shaw, and J.- M. Laberge, “25 years’ experience with lymphangiomas in children,” Journal of Pediatric Surgery, vol. 34, no. 7, pp. 1164–1168, 1999.
• Referans 2- James WD, Burger T, Elston D. Andrews' Diseases of the Skin Clinical Dermatology.10th ed. Saunders Elsevier: United Kingdom; 2011. p.579-82.
• Referans 3- Kim JH, Nam TS, Kim SH. Solitary angiokeratoma developed in one area of lymphangioma circumscriptum. J Korean Med Sci. 1988;3:169-70.
• Referans 4 - Terushkin V, Marmon S, Fischer M, Patel RR, Sanchez MR. Verrucous lymphangioma circumscriptum. Dermatol Online J. 2012;18:9.
• Referans 5- Dermoscopy of cutaneous lymphangioma circumscriptum.Jha AK, Lallas A, Sonthalia S. Dermatol Pract Concept. 2017 Apr 30;7(2):37-38
• Referans 6- Zaballos P, Dauf ı C, Puig S et al. Dermoscopy of solitary angiokeratomas: a morphological study. Arch. Dermatol. 2007;143: 318–25.
• Referans 7- Moscarella E, Zalaudek I, Buccini P et al. Dermoscopy and confocal microscopy of thrombosed hemangiomas. Arch. Dermatol. 2012; 148: 410.
• Referans 8- Patel GA, Schwartz RA. Cutaneous lymphangioma circumscriptum: frog spawn on the skin. Int J Dermatol. 2009;48:1290-5.
• Referans 9- Weigand S, Eivazi B, Zimmerman AP et al. Sclerother-apy of lymphangiomas of the head and neck. HeadNeck 2010;33:1649 –1655.
• Referans 10- Treatment of lymphangioma circumscriptum using fractional carbon dioxide laser ablation. Shumaker PR, Dela Rosa KM, Krakowski AC. Pediatr Dermatol. 2013 Sep-Oct;30(5):584-6.
• Referans 11- K. Niitsuma, M. Hatoko, H. Tada, A. Tanaka, S. Yurugi, and H.Iioka, “Recurrence of cutaneous lymphangioma after surgical resection: Its features and manner,” European Journal of Plastic Surgery, vol. 27, no. 8, pp. 367–370, 2005
• Referans 12- D. T. King, D. M. Duffy, F. M. Hirose, and A. W. Gurevitch,“Lymphangiosarcoma Arising From Lymphangioma Circumscriptum,” JAMA Dermatology, vol. 115, no. 8, pp. 969–972, 1979.
• Referans 13- G. R. Wilson, N. H. Cox, N. R. McLean, and D. Scott, “Squamous cell carcinoma arising within congenital lymphangioma circumscriptum,” British Journal of Dermatology, vol. 129, no. 3,pp. 337–339, 1993
• Referans 14- 14-Shim H, Hecker MS, Phelps RG. Malignant vascular papillary angioendothelioma (Dabska's tumour) arising in a lymphangioma circumscriptum: report ofa case. J Cutan Pathol 1998;25(9):513.