Henoch Schönlein Purpurasının Gastrointestinal Tutulumuyla Seyreden Ailevi Akdeniz Ateşi Vakası

Öz

Henoch Schönlein Purpurası artrit, karın ağrısı, non-trombositopenik purpura ve böbrek tutulumu ile seyreden, çocukluk çağında en sık görülen küçük damar vaskülitidir. Palpabl purpura genelde hastalığın ilk bulgusu olarak ortaya çıkar. Ancak gastrointestinal semptomlar nadiren döküntüden önce ortaya çıkarak tanıda gecikmelere neden olabilmektedir. Bu yazıda akut batın kliniğiyle acil servisimize başvuran, apendektomi yapılan ve klinik takibi sırasında cilt tutulumunun ortaya çıkması ile Henoch Schönlein Purpurası tanısı alan bir vaka sunuyoruz. Vakamızın önemli olan bir diğer noktası da; Henoch Schönlein Purpura atağı sonrasında tekrarlayan karın ağrısı anamnezi olması üzerine yapılan genetik analiz ile hastaya Ailevi Akdeniz Ateşi tanısı konmasıdır.

Anahtar Kelimeler

• Henoch Schönlein Purpurası
• , karın ağrısı
• non-trombositopenik purpura
• Ailevi Akdeniz Ateşi

Familial Mediterranean Fever Present with Gastrointestinal Manifestations of Henoch Schonlein Purpura

Öz

Henoch Schönlein Purpura is the most common small vessel vasculitis in childhood which is characterized with non-thrombocytopenic purpuric skin rash, arthritis, abdominal pain and renal disease. Palpable purpura usually occurs as the first clinical finding. However, gastrointestinal symptoms can rarely appear before the rash and may cause delays in diagnosis. Here, we present a case of Henoch Schönlein Purpura who underwent appendectomy with the diagnosis of acute abdomen and developed skin involvement in clinical follow-up. Another significant point of the case is having anamnesis of recurrent abdominal pain and the diagnosis of Familial Mediterranean Fever by genetic analysis after Henoch Schönlein Purpura attack.

Anahtar Kelimeler

• Henoch Schonlein Purpura
• abdominal pain
• nonthrombocytopenic purpura
• Familial Mediterranean Fever

Kaynakça

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