ORAK HÜCRE ANEMİ KRİZİNE SEKONDER BİLATERAL FEMUR BAŞI OSTEONEKROZUNUN KEMİK SİNTİGRAFİSİ İLE DEĞERLENDİRİLMESİ

Öz

Orak hücreli anemi (Sicklecellanemia) hemoglobin S olarak adlandırılan anormal hemoglobinlerin sebeb olduğu herediter geçişli hastalık olarak tanımlanmaktadır. Orak hücre anemi krizinde genellikle göğüste, kemiklerde ve abdomendeki kapillerlerin morfolojisi bozulmuş eritrositler tarafından tıkanmasıyla meydana gelen infarktlar oluşur. Bu vaka takdimindeorak hücre anemisi bulunan ve bir aydır devam eden yürümekte zorluk ve ağrı şikayeti bulunan 29 yaşında erkek hasta sunulmuştur.Orak hücreli anemi (Sicklecellanemia) hemoglobin S olarak adlandırılan anormal hemoglobinlerin sebeb olduğu vasooklisiv, aplastik ve hemolitik krizlere yol açabilen herediter geçişli bir hastalıktır (1). Orak hücreli anemide akut (ağrılı vasooklisiv kriz) ve kronik olarak (avaskuler nekrozun progresiv olarak ilerlemesi) kemik tutulumu en sık karşılaşılan komplikasyonlardan biridir (2).

Anahtar Kelimeler

• Orak hücre anemisi
• Kemik Sintigrafisi
• Vasooklisiv Kriz

The Evaluation of Bilateral Femoral Head Osteonecrosis Secondary to Sickle Cell Anemia Crisiswith Bone Scintigraphy

Öz

Sicklecellanemia is defined as a hereditary disease which is caused by abnormal hemoglobins that are called hemoglobin S. In sickle cell anemia crisis, generally infarction develops as a result of the blockage of capillaries in the chest, bones and abdomen by the erythrocytes with damaged morphology. In this case presentation, a 29 year old male patient who has sickle cell anemia and who has been experiencing pain and difficulty in walking for a month is chosen. 

Sicklecellanemia is defined as a hereditary disease which is caused by abnormal hemoglobins that are called hemoglobin S. In sickle cell anemia crisis, generally infarction develops as a result of the blockage of capillaries in the chest, bones and abdomen by the erythrocytes with damaged morphology. In this case presentation, a 29 year old male patient who has sickle cell anemia and who has been experiencing pain and difficulty in walking for a month is chosen. 

Anahtar Kelimeler

• Sicklecell anemia
• bone scintigraphy
• vaso-occlusivecrisis

Kaynakça

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