DESENDAN SEYİRLİ BİR GUİLLAİN BARRE SENDROMU OLGUSU

Öz

Guillain Barre Sendromu (GBS), sıklıkla simetrik güçsüzlük ve arefleksi ile karakterize akut inflamatuar polinöropatidir. Geçirilmiş bakteriyel veya viral enfeksiyonların tetiklediği otoimmün bir hastalık olduğu kabul edilmektedir. Çocukluk çağı GBS'de mortalite %1-2 oranındadır ve genellikle solunum yetersizliğine bağlı olarak gelişir. Burada 14 yaşında viral enfeksiyon sonrası GBS gelişen bir erkek çocuk sunularak bu sendromun klinik özellikleri gözden geçirildi.Guillain, Barre ve Strohl 1916’da 1.Dünya Savaşı sırasında iki askerde spontan olarak iyileşen progresif motor bozukluk bildirdiler. Benzer olgular daha önce de bildirilmesine rağmen, Guillain ve ark. reflekslerin bir periferik sinir etkilenmesine bağlı olarak kaybolduğunu ve beyin omurilik sıvısında protein artışıyla birlikte hücre sayısının normal oluşuyla Poliomiyelitten farklı bir hastalık olduğunu gösterdiler (1). 

Anahtar Kelimeler

• Çocuk
• Guillian-Barre Sendromu
• Klinik bulgular

A CASE OF GUILLAIN BARRE SYNDROME WITH DESCENDANT COURSE

Öz

Guillain Barre Syndrome (GBS) is an acute inflammatory polyneuropathy characterized by symmetrical weakness and areflexia. It is considered to be an autoimmune disease triggered by bacterial or viral infections. The mortality is 1-2% in childhood GBS and it usually develops due to respiratory failure. We present a 14 years old boy with GBS developed after viral infection.

Guillain Barre Syndrome (GBS) is an acute inflammatory polyneuropathy characterized by symmetrical weakness and areflexia. It is considered to be an autoimmune disease triggered by bacterial or viral infections. The mortality is 1-2% in childhood GBS and it usually develops due to respiratory failure. We present a 14 years old boy with GBS developed after viral infection.

Anahtar Kelimeler

• Child
• Clinical findings
• Guillain Barre Syndrome

Kaynakça

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