Uterus Didelphys, obstructed hemivagina and ipsilateral renal agenesis: OHRIVA Syndrome

Öz

Herlyn-Werner-Wunderlich syndrome is a rare urogenital anomaly characterized by uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. Patients with this syndrome frequently complain about dysmenorrhea, cyclic abdominal pain, acute abdomen and abdominal mass soon after menarche. İn this case report, we aimed to report a thirteen-year old girl who had Herlyn- Werner Wunderlich Syndrome.Uterus didelphys together with obstructed hemivagina is seen rarely. Although patients with uterus didelphys and obstructed hemivagina are usually asymptomatic until menarche, dysmenorrhea becomes the major complaint after menarche. İn this case report, we aim to present a patient having complaint of dysmenorrhea and diagnosis of Herlyn- Werner Wunderlich Syndrome, characterized by uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis.

Anahtar Kelimeler

• mullerian anomaly
• obstructed hemivagina
• OHRIVA syndrome
• uterus didelphys

UTERUS DIDELFIS, OBSTRÜKTE HEMIVAJEN VE İPSILATERAL RENAL AGENEZI: OHRIVA SENDROMU

Öz

Herlyn-Werner-Wunderlich Sendromu uterus didelfis, obstrükte hemivajen ve ipsilateral renal agenezi ile karakterize nadir görülen bir anomalidir. Bu sendroma sahip hastalar sıklıkla menarştan kısa süre sonra başlayan dismenore, siklik abdominal ağrı, akut abdomen ve abdominal kitleden yakınırlar. Bu olgu sunumunda 13 yaşında Herlyn- Werner Wunderlich Sendromlu bir vaka sunmayı amaçladık.

Herlyn-Werner-Wunderlich Sendromu uterus didelfis, obstrükte hemivajen ve ipsilateral renal agenezi ile karakterize nadir görülen bir anomalidir. Bu sendroma sahip hastalar sıklıkla menarştan kısa süre sonra başlayan dismenore, siklik abdominal ağrı, akut abdomen ve abdominal kitleden yakınırlar. Bu olgu sunumunda 13 yaşında Herlyn- Werner Wunderlich Sendromlu bir vaka sunmayı amaçladık

Anahtar Kelimeler

• mülleryan anomali
• obsrükte hemivajen
• OHRIVA sendromu
• uterus didelfis

Kaynakça

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