Primer Lokalize Kutanöz Amiloidoz ve Diffüz Sistemik Skleroz Birlikteliği: Olgu Sunumu

Yıl 2018, Cilt: 5 Sayı: 3, 37 - 38, 04.12.2018

Emine Figen Tarhan , Emine Koca

Öz

Primer lokalize kutanöz amiloidoz ve diffüz
sistemik skleroz birlikteliği nadirdir. 15 yıl önce biyopsi ile primer lokalize
kutanöz amiloidoz tanısı alan 61 yaşındaki bir kadın hastaya deri ve lokomotor
sistem bulguları, kapilleroskopi bulguları ve otoantikor (anti-Scl-70)
pozitifliği ile diffüz sistemik skleroz tanısı konulmuştur. Farklı klinik,
etiyopatogenetik ve genetik özellikleri olan bu iki hastalık nadiren bir arada
görülmektedir.

Anahtar Kelimeler

Amiloidozis, CREST, Sistemik Skleroz

Co-existence of Primary Localized Cutaneous Amyloidosis and Diffuse Systemic Sclerosis: Case Report

Öz

Co-existence of
primary localized cutaneous amyloidosis and diffuse systemic sclerosis is very
rare. In a 61-year-old woman who was diagnosed as primary localized cutaneous
amyloidosis with biopsy 15 years ago, additional diagnosis of diffuse systemic
sclerosis was made based upon skin, locomotor system and capilloroscopy findings
and autoantibody (anti- Scl70) positivity. These two autoimmune diseases, which
have different aetiopathogenesis as well as diverse clinical and genetic
characteristics, are rarely seen together.

Anahtar Kelimeler

Amyloidosis, CREST, Systemic Sclerosis

Kaynakça

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