A case report of Dyke Davidoff Masson syndrome which is diagnosed in advanced age

Yıl 2016, Cilt: 8 Sayı: 4, 222 - 226, 01.12.2016

Ümmü Serpil Sarı , Ecenur Aydın Aşık Ayşin Kısabay Hatice Mavioğlu

https://doi.org/10.21601/ortadogutipdergisi.273597

Öz

Major findings of
Dyke-Davidoff-Masson syndrome (DDMS) are unilateral cerebral atrophy,
contralateral hemiparesis and seizures. DDMS is a cranial malformation which is
described by Dyke and his colleagues in 1933. The etiology of DDMS are trauma,
inflamation, vascular malformations and occlusions. Computerized tomography and
magnetic resonance imaging are the gold standard for diagnosis of DDMS.

In this publication, we want to
emphasize DDMS once more with the rare case of a 55 years old female patient
who had a history of epilepsy since age of 4 
and has epilepsy and facial asymmetry, hemidystonia, mental retardation,
cranial hemiatrophy findings and DDMS diagnosis in advanced age. 

Anahtar Kelimeler

Dyke Davidoff Masson syndrome, hemidystonia, seizure

İleri yaşta tanı konulan bir Dyke Davidoff Masson sendromu olgu sunumu

Öz

Dyke-Davidoff-Masson sendromu (DDMS)
major bulguları unilateral serebral atrofi, kontrolateral hemiparazi ve
nöbetlerle karakterize, ilk kez Dyke  ve
arkadaşları tarafından 1933 yılında  
tanımlanan bir kranial malformasyondur. DDMS sendromunun etiyolojisi
travma, inflamasyon, vasküler malformasyonlar 
ve oklüzyonları içerir. Tanıda altın standart kranial bilgisayarlı
tomografi ve manyetik rezonans görüntülemedir.

Bu yazıda 4 yaşından
beri epilepsi tanısıyla tedavi gören 55 yaşındaki bayan hastanın epilepsiye
eşlik eden fasial asimetri,  hemiparezi,
hemidistoni, mental retardasyon, kraniyal hemiatrofi  bulguları ile ileri yaşta DDMS  tanısı alması nedeniyle nadiren görülen bu
sendromu olgu ve literatür eşliğinde vurgulamak istedik.

Anahtar Kelimeler

Dyke Davidoff Masson sendromu, hemidistoni, nöbet

Kaynakça

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