A Different Clinical Presentation for Intestinal Obstruction due to Rapunzel Syndrome: Diarrhea

Yıl 2021, Cilt: 6 Sayı: 1, 143 - 149, 05.03.2021

Aytaç Taşcı Turan Yıldız

https://doi.org/10.26453/otjhs.844272

Öz

Trichobezoars are defined as accumulation of hair or hair like substances in the stomach and/or small intestinal. It’s called Rapunzel syndrome when the accumulated hair ball pass the pylorus and reaches the small intestines and colon from the stomach. Clinical findings and treatment methods may vary according to the localization and size of the hair ball. In the literature; there are a limited of number publications about trichobezoar and Rapunzel syndrome but there hasn’t been a report of intestinal obstruction due to trichobezoar presenting to the emergency department with diarrhea. In this report; we will present a patient who applied to the emergency department with diarrhea and vomiting associated with intestinal obstruction due to Rapunzel syndrome.

Anahtar Kelimeler

Rapunzel syndrome, trichobezoars,, intestinal obstruction

Rapunzel Sendromuna Bağlı İntestinal Obstrüksiyonun Farklı Bir Klinik Sunumu: İshal

Öz

TTrikobezoar yutulan saç veya saç benzeri maddelerin mide ve/veya ince barsakda birikimine denilir. Midede biriken saç topunun nadiren de olsa piloru geçerek ince barsaklara hatta kolona ulaşmasına Rapunzel sendromu denilmektedir. Klinik bulgular ve tedavi yöntemleri saç topunun büyüklük ve konumuna göre değişmektedir. Literatürde trikobezoarlar hakkında sınırlı sayıda yayın olmak ile beraber trikobezoar nedeniyle gelişen intestinal obstrüksiyon sonrası ishal ile acil servise başvuru hakkında yayın yoktur. Yazımızda acil servisimize Rapunzel sendromuna bağlı intestinal obstrüksiyon sonrası ishal ve kusma ile başvuran bir hastayı sunacağız.

Anahtar Kelimeler

Rapunzel sendromu,, trikobezoar,, intestinal obstrüksiyon

Kaynakça

• Gonuguntla V, Joshi DD. Rapunzel syndrome: a comprehensive review of an unusual case of trichobezoar. Clin Med Res. 2009;7:99-102.
• Naik S, Gupta V, Naik S, Rangole A, Chaudhary AK, Jain P. Rapunzel syndrome reviewed and redefined. Dig Surg. 2007;24:157-161.
• Armstrong JH, Holtzmuller KC, Barcia PJ. Gastric trichobezoar as a manifestation of child abuse. Curr Surg. 2001;58:202-204.
• Mehta MH, Patel RV. Intussusception and intestinal perforations caused by multiple trichobezoars. J Pediatr Surg. 1992;27:1234-1235.
• Kilincaslan H, Aydoğdu I, Kucukkoc M Osmanoglu NK, Karacanoglu D. Approach to trichobezoar cases in children: Literature review. Bezmialem Science. 2014;2:26-30.
• Cannalire G, Conti L, Celoni M, et al. Rapunzel syndrome: an infrequent cause of severe iron deficiency anemia and abdominal pain presenting to the pediatric emergency department BMC Pediatrics. 2018;125:1097-1098.
• Erzurumlu K, Malazgirt Z, Bektas A, Dervisoglu A. Gastrointestinal bezoars: A retrospective analysis of 34 cases. World J Gastroenterol. 2005;11(12):1813-1817.
• Maglinte DD, Heitkamp DE, Howard TJ, Frederick MK. Lappas JC. Current concepts in imaging of small bowel obstruction. Radiol Clin North Am. 2003;41(2):263-283.
• Tudor ECG, Clark MC. Laparoscopic-assisted removal of gastric trichobezoar; a novel technique to reduce operative complications and time. J. Pediatr. Surg. 2013;48(3):13-15.
• Gülerman F, Güven B, Demir S, Özmen İ. How should trichobezoar be treated in children? Turk J Gastroenterol. 2019;30(7):660-661.