Pediatrik pineal ve tektal bölge tümörleri: nöroendoskopi kullanımı

Öz

Amaç: Bu yazıda kliniğimizde endoskopik girişimlerle tedavi edilen pediatrik pineal ve tektal kitlelere yaklaşımımızı anlatarak literatüre katkıda bulunmayı amaçladık. Gereç ve yöntem: Gazi Üniversitesi Çocuk Nöroşirürji Bilim Dalı'nda 2012-2023 yılları arasında pineal ve tektal bölgede lezyonu olan ve endoskopik girişim uygulanan 26 hastanın kayıtları retrospektif olarak incelendi. Demografik veriler, kan tümör belirteçleri (alfa fetoprotein-BETA AFP, alfa fetoprotein-β-hCG), patolojik tanılar, klinik başvuru nedenleri, hidrosefali varlığı ve ek girişimler analiz edildi. Bulgular: Endoskopik işlem uygulanan 26 hastanın 6'sında pineal bölgede, 20'sinde ise tektal bölgede lezyon vardı. ETV için başarı oranı %75-80 idi. ETV için başarı oranı pineal bölgede tümörü olan hastalar için %78,3 ve tektal tümörler için %84 idi. Sonuç: Pineal veya tektal bölge tümörleri nadir görülen bir tümör grubudur. Ayrıca bu bölgeler tümör tipi ve histolojisi açısından santral sinir sistemindeki en heterojen bölgeler arasındadır. Rijit endoskopi kullanılarak tek bir burr deliğinden endoskopik girişim, endikasyonu olan vakalarda aynı seansta hem patolojik örnekleme hem de hidrosefali yönetimi için konforlu ve güvenli bir minimal invaziv yöntemdir.

Anahtar Kelimeler

• Pediatrik tümörler
• pineal tümörler
• tektal tümörler
• nöroendoskopi

Pediatric pineal and tectal region tumors: the use of neuroendoscopy

Öz

Purpose: In this article, we aimed to contribute to the literature by describing our approach to pediatric pineal and tectal masses treated with endoscopic interventions in our clinic. Materials and methods: We retrospectively reviewed the records of 26 patients with lesions in the pineal and tectal regions who underwent endoscopic procedures between 2012 and 2023 at Gazi University Department of Pediatric Neurosurgery. Demographic data, blood tumor markers (alpha fetoprotein-BETA AFP, alpha fetoprotein-β-hCG), pathological diagnoses, reasons for clinical presentation, presence of hydrocephalus and additional interventions were analyzed. Results: Of the 26 patients who underwent endoscopic procedure, 6 had lesions in the pineal region and 20 had lesions in the tectal region. The success rate for ETV was 75-80%. The success rate for ETV was 78.3% for patients with tumors in the pineal region and 84% for tectal tumors. Conclusion: Pineal or tectal region tumors are a rare group of tumors. In addition, these regions are among the most heterogeneous regions in the central nervous system in terms of tumor type and histology. Endoscopic intervention through a single burr hole using rigid endoscopy is a comfortable and safe minimally invasive method for both pathologic sampling and management of hydrocephalus in indicated cases in the same session.

Anahtar Kelimeler

• Pediatric tumors
• pineal tumors
• tectal tumors
• neuroendoscopy

Kaynakça

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