Ailesel Akdeniz Ateşi

Yunus Ugan; Fatih Ermiş

doi:10.17343/sdutfd.58431

Ailesel Akdeniz Ateşi

Öz

Ailesel Akdeniz Ateşi tekrarlayan ateş ve serozit ataklarıyla karakterize otozomal resesif geçişli otoinflamatuar bir hastalıktır. Hastalığa 16. kromozomun kısa kolunda yer alan ve MEFV olarak isimlendirilen genin neden olduğu bilinmektedir. Bugüne kadar 150'den fazla gen mutasyonu tanımlanmış olmasına rağmen hastalığın tanısı halen klinik olarak konulmaktadır. Hastalığın en önemli ve prognozu belirleyen komplikasyonu amiloidozdur. Hem amiloidoz gelişimini engelleyen hem de atak şiddeti ve sıklığını azaltan tek tedavi ajanı kolşisindir. Bu derlemede, bu tarihi hastalıkla ilgili en son bilgileri gözden geçirmeyi amaçladık.

Anahtar Kelimeler

Ailesel Akdeniz Ateþi, Ateþ, Kolþisin, Amiloidoz

Kaynakça

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Ayrıntılar

Birincil Dil

İngilizce

Konular

-

Bölüm

-

Yazarlar

Yunus Ugan

Fatih Ermiş

Yayımlanma Tarihi

30 Aralık 2011

Gönderilme Tarihi

16 Haziran 2011

Kabul Tarihi

-

Yayımlandığı Sayı

Yıl 2011 Cilt: 18 Sayı: 4

DOI

https://doi.org/10.17343/sdutfd.58431

IZ

https://izlik.org/JA25MN79PA

Kaynak Göster

RIS / Bibtex

APA

Ugan, Y., & Ermiş, F. (2011). Ailesel Akdeniz Ateşi. Medical Journal of Süleyman Demirel University, 18(4), 139-143. https://doi.org/10.17343/sdutfd.58431

AMA

1.Ugan Y, Ermiş F. Ailesel Akdeniz Ateşi. SDÜ Tıp Fak Derg. 2011;18(4):139-143. doi:10.17343/sdutfd.58431

Chicago

Ugan, Yunus, ve Fatih Ermiş. 2011. “Ailesel Akdeniz Ateşi”. Medical Journal of Süleyman Demirel University 18 (4): 139-43. https://doi.org/10.17343/sdutfd.58431.

EndNote

Ugan Y, Ermiş F (01 Aralık 2011) Ailesel Akdeniz Ateşi. Medical Journal of Süleyman Demirel University 18 4 139–143.

IEEE

[1]Y. Ugan ve F. Ermiş, “Ailesel Akdeniz Ateşi”, SDÜ Tıp Fak Derg, c. 18, sy 4, ss. 139–143, Ara. 2011, doi: 10.17343/sdutfd.58431.

ISNAD

Ugan, Yunus - Ermiş, Fatih. “Ailesel Akdeniz Ateşi”. Medical Journal of Süleyman Demirel University 18/4 (01 Aralık 2011): 139-143. https://doi.org/10.17343/sdutfd.58431.

JAMA

1.Ugan Y, Ermiş F. Ailesel Akdeniz Ateşi. SDÜ Tıp Fak Derg. 2011;18:139–143.

MLA

Ugan, Yunus, ve Fatih Ermiş. “Ailesel Akdeniz Ateşi”. Medical Journal of Süleyman Demirel University, c. 18, sy 4, Aralık 2011, ss. 139-43, doi:10.17343/sdutfd.58431.

Vancouver

1.Yunus Ugan, Fatih Ermiş. Ailesel Akdeniz Ateşi. SDÜ Tıp Fak Derg. 01 Aralık 2011;18(4):139-43. doi:10.17343/sdutfd.58431