Kartagener sendromu: olgu sunumu

Year 2005, Volume: 12 Issue: 1, 61 - 64, 03.04.2009

H.Ahmet Bircan Özlem Kaya Ahmet Akkaya Ünal Şahin

Abstract

SüleymanDemirel Üniversitesi
TIP FAKÜLTESİ DERGİSİ: 2005 Mart; 12(1)



Kartagener sendromu: olgu sunumu


H. Ahmet Bircan, Özlem Kaya, Ahmet Akkaya, Ünal Şahin



Özet

Kartagener sendromu; bronşektazi, situs inversus ve paranazal sinuzit triadını içeren otozomal resesif geçiş gösteren genetik bir hastalıktır. Kliniğimize öksürük, pürülan balgam, nefes darlığı, yakınmalarıyla başvuran bayan olguda klinik ve radyolojik olarak Kartagener sendromu tanısı konuldu. Hastadan alınan balgam örneğinden Escherichia coli üretildi. Bronşektazi olgularında Escherichia coli'nin neden olduğu pulmoner enfeksiyonlar kliniklerde nadiren görülmektedir. Yıllarca tekrarlayan pnömonilere neden olması, göreceli nadirliği nedeniyle olguyu sunmayı uygun gördük.



Anahtar kelimeler: Kartagener sendromu, bronşektazi, pnömoni, Escherichia coli



Abstract



Kartagener syndrome: a case report

Kartagener's syndrome, the triad of situs inversus, paranasal sinusitis, and bronchiectasis, is a genetic disease inherited as an autosomal recessive trait. Kartagener syndrome was diagnosed at patient submitted to our clinic with the symptoms such as productive cough, purulent sputum and shortness of breath. Escherichia coli were isolated from sputum of our patient. In clinical settings, pulmonary infection due to E.coli in bronchiectatic patients is rare. Because of relative rarity of this disease that caused recurrent pneumonia for many years we approved to report this case.



Key words: Kartagener's syndrome, bronchiectasis, pneumonia, Escherichia coli

Keywords

Kartagener sendromu, bronþektazi, pnömoni, Escherichia coli

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