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Kartagener sendromu: olgu sunumu

Year 2005, Volume: 12 Issue: 1, 61 - 64, 03.04.2009

Abstract

SüleymanDemirel Üniversitesi
TIP FAKÜLTESİ DERGİSİ: 2005 Mart; 12(1)



Kartagener sendromu: olgu sunumu


H. Ahmet Bircan, Özlem Kaya, Ahmet Akkaya, Ünal Şahin



Özet

Kartagener sendromu; bronşektazi, situs inversus ve paranazal sinuzit triadını içeren otozomal resesif geçiş gösteren genetik bir hastalıktır. Kliniğimize öksürük, pürülan balgam, nefes darlığı, yakınmalarıyla başvuran bayan olguda klinik ve radyolojik olarak Kartagener sendromu tanısı konuldu. Hastadan alınan balgam örneğinden Escherichia coli üretildi. Bronşektazi olgularında Escherichia coli'nin neden olduğu pulmoner enfeksiyonlar kliniklerde nadiren görülmektedir. Yıllarca tekrarlayan pnömonilere neden olması, göreceli nadirliği nedeniyle olguyu sunmayı uygun gördük.



Anahtar kelimeler: Kartagener sendromu, bronşektazi, pnömoni, Escherichia coli



Abstract



Kartagener syndrome: a case report

Kartagener's syndrome, the triad of situs inversus, paranasal sinusitis, and bronchiectasis, is a genetic disease inherited as an autosomal recessive trait. Kartagener syndrome was diagnosed at patient submitted to our clinic with the symptoms such as productive cough, purulent sputum and shortness of breath. Escherichia coli were isolated from sputum of our patient. In clinical settings, pulmonary infection due to E.coli in bronchiectatic patients is rare. Because of relative rarity of this disease that caused recurrent pneumonia for many years we approved to report this case.



Key words: Kartagener's syndrome, bronchiectasis, pneumonia, Escherichia coli

References

  • Swartz MN. Bronchiectasis. In: Fishman AP (ed). Fishman’s Pulmonary Diseases and Disorders. 3rd Ed. Newyork, McGraw-Hill Comp., 1998; 2045-70.
  • Kaya A, Kaya SU, Fitoz S, Tuncalý T, Gönüllü U. Kartagener Sendromu: Üç olgu sunumu. Toraks Dergisi 2002; 3: 113-6.
  • Seaton A, Seaton D, Leýtch AG. Crofton and Douglas’s Respiratory Diseases. 4th ed. London, Blackwell Scientific Publications, 1989; 601-3.
  • Þenyiðit A, Asan E, Kandemir N, Özateþ M, Çoþkunsel M. Kartagener Sendromu (3 Olgu Nedeniyle). Dicle Üniversitesi Týp Fakültesi Dergisi. 1997; 24: 139-45.
  • Lungarella G, De Santi MM, Palatresi R, Tosi P. Ultrastructural observations on basal apparatus of respiratory cilia in immotile cilia syndrome. Eur J Respir Dis. 1985; 66(3): 165-72.
  • Eavey RD, Nadol JB Jr, Holmes LB, Laird NM, Lapey A, Joseph MP, et al. Kartagener’s syndrome. A blinded, controlled study of cilia ultrastructure. Arch Otolaryngol Head Neck Surg 1986;112(6): 646-50.
  • Schwarzenberg H, Elfeldt RJ, Schluter E, Link J, Heller M. Severe Hemoptysis Requiring Lobectomy in an 11-Year-Old Patient With Kartagener’s Syndrome. Ann Thorac Surg. 1997; 64(3): 852-4.
  • Greenstone M, Stanley P, Cole P, Mackay I. Upper airway manifestations of primary ciliary dyskinesia. J Laryngol Otol 1985; 99(10): 985-91.
  • Mygind N, Pedersen M. Nose-, sinus- and ear-symptoms in 27 patients with primary ciliary dyskinesia. Eur J Respir Dis Suppl 1983; 127: 96-101.
  • Nadel HR, Stringer DA, Levison H, Turner JA, Sturgess JM. The immotile cilia syndrome: radiological manifestations. Radiology 1985; 154(3): 651-5.
  • Eisenstein BI. Enterobacteriaceae. In: Mandell GL, Bennett JE, Dolin R. (eds). Principles and Practise of Infectious Diseases. 4th Ed. Philadelphia, Churchill Livingstone, 1995; 1969-72.
  • Bjerkestrand G, Digranes A, Schreiner A. Bacteriological findings in transtracheal aspirates from patients with chronic bronchitis and bronchiectasis: a preliminary report. Scand J Respir Dis 1975; 56: 201- 7.
  • Tillotson JR, Lerner AM. Characteristics of pneumonias caused by Escherichia coli. N Engl J Med. 1967; 277: 115-22.
  • Wang JY, Hsueh PR, Wang JT, Lee LN, Yang PC, Luh KT. Recurrent infections and chronic colonization by an Escherichia coli clone in the respiratory tract of a patient with severe cystic bronchiectasis. J Clin Microbiol. 2000; 38(7): 2766-7.
Year 2005, Volume: 12 Issue: 1, 61 - 64, 03.04.2009

Abstract

References

  • Swartz MN. Bronchiectasis. In: Fishman AP (ed). Fishman’s Pulmonary Diseases and Disorders. 3rd Ed. Newyork, McGraw-Hill Comp., 1998; 2045-70.
  • Kaya A, Kaya SU, Fitoz S, Tuncalý T, Gönüllü U. Kartagener Sendromu: Üç olgu sunumu. Toraks Dergisi 2002; 3: 113-6.
  • Seaton A, Seaton D, Leýtch AG. Crofton and Douglas’s Respiratory Diseases. 4th ed. London, Blackwell Scientific Publications, 1989; 601-3.
  • Þenyiðit A, Asan E, Kandemir N, Özateþ M, Çoþkunsel M. Kartagener Sendromu (3 Olgu Nedeniyle). Dicle Üniversitesi Týp Fakültesi Dergisi. 1997; 24: 139-45.
  • Lungarella G, De Santi MM, Palatresi R, Tosi P. Ultrastructural observations on basal apparatus of respiratory cilia in immotile cilia syndrome. Eur J Respir Dis. 1985; 66(3): 165-72.
  • Eavey RD, Nadol JB Jr, Holmes LB, Laird NM, Lapey A, Joseph MP, et al. Kartagener’s syndrome. A blinded, controlled study of cilia ultrastructure. Arch Otolaryngol Head Neck Surg 1986;112(6): 646-50.
  • Schwarzenberg H, Elfeldt RJ, Schluter E, Link J, Heller M. Severe Hemoptysis Requiring Lobectomy in an 11-Year-Old Patient With Kartagener’s Syndrome. Ann Thorac Surg. 1997; 64(3): 852-4.
  • Greenstone M, Stanley P, Cole P, Mackay I. Upper airway manifestations of primary ciliary dyskinesia. J Laryngol Otol 1985; 99(10): 985-91.
  • Mygind N, Pedersen M. Nose-, sinus- and ear-symptoms in 27 patients with primary ciliary dyskinesia. Eur J Respir Dis Suppl 1983; 127: 96-101.
  • Nadel HR, Stringer DA, Levison H, Turner JA, Sturgess JM. The immotile cilia syndrome: radiological manifestations. Radiology 1985; 154(3): 651-5.
  • Eisenstein BI. Enterobacteriaceae. In: Mandell GL, Bennett JE, Dolin R. (eds). Principles and Practise of Infectious Diseases. 4th Ed. Philadelphia, Churchill Livingstone, 1995; 1969-72.
  • Bjerkestrand G, Digranes A, Schreiner A. Bacteriological findings in transtracheal aspirates from patients with chronic bronchitis and bronchiectasis: a preliminary report. Scand J Respir Dis 1975; 56: 201- 7.
  • Tillotson JR, Lerner AM. Characteristics of pneumonias caused by Escherichia coli. N Engl J Med. 1967; 277: 115-22.
  • Wang JY, Hsueh PR, Wang JT, Lee LN, Yang PC, Luh KT. Recurrent infections and chronic colonization by an Escherichia coli clone in the respiratory tract of a patient with severe cystic bronchiectasis. J Clin Microbiol. 2000; 38(7): 2766-7.
There are 14 citations in total.

Details

Primary Language English
Journal Section Olgu Sunumları
Authors

H.Ahmet Bircan This is me

Özlem Kaya This is me

Ahmet Akkaya This is me

Ünal Şahin This is me

Publication Date April 3, 2009
Submission Date April 3, 2009
Published in Issue Year 2005 Volume: 12 Issue: 1

Cite

Vancouver Bircan H, Kaya Ö, Akkaya A, Şahin Ü. Kartagener sendromu: olgu sunumu. Med J SDU. 2009;12(1):61-4.

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