Primer intrakardiyak tümörler klinik pratikte nadir görülür ve otopsi serilerinde sıklığının %0.3’ten daha az olduğu bildirilmiştir. Bunların yaklaşık %50’si kardiyak miksomalardır. Papiller fibroelastomlar, kardiyak miksomalardan sonra ikinci en sık görülen primer kardiyak tümörlerdir ve genellikle kalp kapaklarını tutar ve onlara zarar verir. Bu tümörler asemptomatik seyredebileceği gibi ani kardiyak ölüm gibi ciddi sonuçlarla da ilişkili olabilirler. Biz bu vakada, tekrarlayan akut pulmoner ödem ile prezente olan ve mitral arka kapakta papiller fibroelastom tanısı alan 77 yaşında bir erkek hastayı sunduk.
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Aslan AN, Baştuğ S, Ertem AG, Turinay ZŞ, Bayram H, Güney MC, Bozkurt E. A Huge Papillary Fibroelastoma Case Presenting with Recurrent Acute Pulmonary Edema. Sakarya Tıp Dergisi. Haziran 2016;6(2).