Çocuklarda Nadir Bir Şilotoraks Nedeni: Gorham-Stout Sendromu

Engin Aydın

doi:10.12956/tjpd.2018.375

Olgu Sunumu

A Rare Cause of Chylothorax in Children: Gorham-Stout Syndrome

Yıl 2019, , 36 - 39, 21.03.2019

Engin Aydın

https://doi.org/10.12956/tjpd.2018.375

Öz

Gorham-Stout disease is a complex disease in which lytic lesions of bone tissue are accompanied by chylothorax and abdominal lymphangioma. The etiology is still unknown. The diagnosis is made by the patient’s clinical and laboratory findings and biopsy results. It may be fatal depending on the organs involved. Although many treatments have been described, successful results have been reported with interferon alpha 2b in recent years. We discuss the clinical diagnosis and treatment of a 5-year-old female patient with osteolytic lesions in the bones after she was referred with chylothorax

Anahtar Kelimeler

Child, Gorham-Stout Syndrome, Interferon Alfa-2b

Kaynakça

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