Çıkan Aortadan Anormal Kaynaklanan Sağ Pulmoner Arter, Aortopulmoner Pencere ve Kesintili Arkus Aorta Birlikteliği: Tek 3d Yama ile Başarılı Cerrahi Düzeltme

Öz

Çıkan aortadan anormal kaynaklanan sağ pulmoner arter (ÇAAKPA) nadir görülen bir konjenital kalp defekti olup genellikle başka kalp anomalilerine eşlik eder. ÇAAKPA’lı hastalarda artmış pulmoner kan akımı sonucunda konjestif kalp yetmezliği ve tek taraflı pulmoner hipertansiyon gelişir. Bu nedenle cerrahi düzeltme yapılmayan hastalar genellikle yenidoğan ya da erken süt çocukluğu döneminde hayatını kaybederler. Bu yazıda, ÇAAKPA, aortopulmoner pencere ve kesintili arkus aorta birlikteliği saptanan ve tek 3D ksenograft yama kullanılarak başarılı bir şekilde opere edilen 1.5 aylık kız hasta sunulmaktadır.

Anahtar Kelimeler

• Çıkan aortadan anormal kaynaklanan sağ pulmoner arter, Aortopulmoner pencere, Konjenital kalp hastalığı, Kesintili arkus aorta

Anomalous Origin of the Right Pulmonary Artery from Ascending nomalous Origin of the Right Pulmonary Artery from Ascending Aorta Associated with Aortopulmonary Window and Interrupted orta Associated with Aortopulmonary Window and Interrupted Aortic Arch: Successful Surgical Correction with a Single 3 ortic Arch: Successful Surgical Correction with a Single 3D Patch

Öz

Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare congenital heart defect and generally associated with other cardiac anomalies. Patients with AORPA have high pulmonary fl ow results in congestive heart failure and unilateral pulmonary hypertension. Thus, it is frequently a fatal malformation in the neonatal or early infancy periods if early surgical repair is not performed. Herein, we report a 1.5 month-old girl who was diagnosed with AORPA associated with aortopulmonary window and interrupted aortic arch and successfully operated using a single pericardial xenograft 3D patch

Anahtar Kelimeler

• Anomalous origin of the right pulmonary artery from ascending aorta, Aortopulmonary window, Congenital heart defect, Interrupted aortic arch

Kaynakça

1. Penkoske PA, Castaneda AR, Fyler DC, Van Praagh R. Origin of pulmonary artery branch from ascending aorta. J Thorac Cardiovasc Surg 1983;85:537–45.
2. Kutsche LM, Van Mierop LH. Anomalous origin of a pulmonary artery from the ascending aorta: Associated anomalies and pathogenesis. Am J Cardiol 1988;61:850-6.
3. Abu-Sulaiman RM, Hashmi A, McCrindle BW, Williams WG, Freedom RM. Anomalous origin of one pulmonary artery from the ascending aorta: 36 years’ experience from one centre. Cardiol Young 1998;8:449-54.
4. Prifti E, Bonacchi M, Murzi B, Crucean A, Leacche M, Bernabei M, et al. Anomalous origin of the right pulmonary artery from the ascending aorta. J Card Surg 2004;19:103-12.
5. Cinar A, Haliloglu M, Karagoz T, Karcaaltincaba M, Celiker A, Tekinalp G. Interrupted aortic arch in a neonate: Multidetector CT diagnosis. Pediatr Radiol 2004;34:901-3.
6. Garg P, Talwar S, Kothari SS, Saxena A, Juneja R, Choudhary SK, et al. The anomalous origin of the branch pulmonary artery from the ascending aorta. Interact Cardiovasc Thorac Surg 2012;15: 86-92.