Peliosis Hepatis Gelişen Bir Fanconi Aplastik Anemi Olgusu

Yıl 2010, Cilt: 4 Sayı: 3, 171 - 174, 01.06.2010

Ali Bay Neşe Yaralı Serdar Özkasap Pamir Işık Abdurrahman Kara Suat Fitöz Bahattin Tunç

Öz

Peliosis hepatis karaciğerin değişik etiyolojik faktörler ve farklı patogenetik mekanizmalara bağlı olarak gelişen nadir bir vasküler hastalığıdır. Kemik iliği yetmezliği sendromlarında sıklıkla kullanılan androjenler nadiren peliosis hepatise neden olabilirler. Biz Fanconi aplastik anemi tanısı ile 4 yıldır androjen kullanan ve peliosis hepatis gelişen bir olguyu sunduk.

Anahtar Kelimeler

Peliosis hepatis , aplastik anemi , androjen

A PATIENT WITH FANCONI APLASTIC ANEMIA DEVELOPED PELIOSIS HEPATIS

Öz

Peliosis hepatis (PH) is an uncommon vascular disorder of the liver that may be caused by several etiologic agents and different pathogenetic mechanisms. Androgens which are widely used in the treatment of bone marrow failure syndromes can cause hepatic peliosis in rare cases. We describe a case of Fanconi aplastic anaemia in which PH developed after 4 years of treatment with androgens

Anahtar Kelimeler

Peliosis hepatis , aplastic anaemia , androgen

Kaynakça

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