Nörogörüntülemede Multipl Skleroz İle Karışan Bir Hastalık: Nöro-Behçet

Yıl 2013, Özel Sayı, 47 - 49, 01.06.2013

Yasemin Topçu Erhan Bayram Gülçin Akıncı Erbil Ünsal Semra Hiz Kurul

Öz

Akut izole nörolojik sendrom multipl sklerozun en sık görülen semptomudur ve antifosfolipid sendromu, sistemik lupus eritematozus, Nöro-Behçet gibi hastalıkların ilk bulgusu olarak ortaya çıkabilmektedir. Demiyelinizan bulguları olan hastalar ise yanlışlıkla mutipl skleroz olarak değerlendirilebilmektedirler. Nöro-Behçet hastalığı manyetik rezonans görüntüleme bulguları ve klinik seyir açısından multipl skleroza benzeyebilen inflamatuvar bir hastalıktır. Burada demiyelinizan özellikleri bulunan hastaların ayırıcı tanısında akılda tutulması gerekliliğini vurgulamak ve nadir görülmesi açısından nöro-Behçet hastalığı tanısı alan 13 yaşında kız olgu sunuldu.

Anahtar Kelimeler

Behçet hastalığı, Çocukluk çağı, Multipl skleroz, Nöro-Behçet, Nörogörüntüleme

A Disease Confused with Multiple Sclerosis in Neuroimaging: Neuro-Behçet

Öz

Acute isolated neurological syndrome is the most common symptom in multiple sclerosis but can also be the only feature or first manifestation in antiphospholipid syndrome, systemic lupus erythematosus and neuro-Behçet’s disease. Patients with demyelinating features may be given the false label of multiple sclerosis. Neuro-Behçet’s disease is an inflammatory disorder where the magnetic resonance imaging findings and clinical course may mimic multiple sclerosis. Here we present a 13 year-old girl with neuro-Behçet’s disease in terms of rarity and review of the differential diagnosis of demyelinating features

Anahtar Kelimeler

Behçet’s disease, Childhood, Multiple sclerosis, Neuro-Behçet, Neuroimaging

Kaynakça

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