Adrenokortikal Tümöre Bağlı Cushing Sendromu: Olgu Sunumu

Yıl 2007, Cilt: 1 Sayı: 2, 42 - 45, 01.04.2007

Pınar İşgüven Metin Yıldız Ayla Güven Müferet Ergüven Mehmet Malçok Pelin Bağcı

Öz

Adrenokortikal tümörler (AKT) pediatrik yaş grubunda nadirdir. Çok sıklıkla görülmedikleri için patogenezleri, prognozları, ve tedavi yöntemleri hala net değildir. Adrenokortikal tümörlü çocuklar sıklıkla cushingoid semptomlar ve virilizasyon gibi endokrin bozukluk belirti ve bulguları gösterirler. Burada, bir aydır cushingoid semptomları olan ve adrenokortikal tümör saptanan ikiaylık bir kız çocuğu sunulmaktadır.

Anahtar Kelimeler

Cushing sendromu, adrenokortikal tümör

CUSHING'S SYNDROME CAUSED BY ADRENOKORTİKAL TUMOR: Case Report

Öz

Adrenokortikal tumors (ACTs) are rare in the pediatric population. The pathogenesis, prognostic
indicators, and manegement of these tumors are still unclear due to low prevalence. Most children
with an ACT present with sign and syptoms of endocrine disturbances including cuhingoid
symtoms and virilization. Here, we report a 2 month-old girl with cushingoid symptoms and
diagnosed as adrenocortical tumor

Anahtar Kelimeler

Cushing syndrome, adrenocortical tumor

Kaynakça

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