Telengiectasia Macularis Eruptiva Perstans: A Case Report

Yıl 2014, Cilt: 21 Sayı: 3, 229 - 232, 01.06.2014

Mahmut Sami Metin Ömer Faruk Elmas Okan Kızılyel Betül Gündoğdu Necmettin Akdeniz

Öz

Cutaneous mastocytosis is a group of diseases characterized by infiltration of mast cells in the skin. Telengiectasia macularis eruptiva perstans is a rare form of cutaneous mastocytosis and it is usually seen in adults. Round, oval, brown-red macular lesions are usually seen on the trunk. Systemic involvement may be observed in one third of the patients. Treatment depends on the presence of systemic involvement and clinical symptoms of patients. Our patient was a 39 years old man presented with widespread brownish pruritic macular lesions on his trunk and arms. There was no systemic involvement. The patient was diagnosed with telengiectasia macularis eruptiva perstans both clinically and histopathologically. We decided to report this case because telengiectasia macularis eruptiva perstans is an atypical form of cutaneous mastocytosis and is rarely seen. Key words: Cutaneous Mastocytosis; Systemic Involvement; Telengiectasia Macularis Eruptiva Perstans.

Anahtar Kelimeler

Cutaneous Mastocytosis; Systemic Involvement; Telengiectasia Macularis Eruptiva Perstans.

Telenjiektazia makülaris erüptiva perstans: Bir olgu sunumu

Öz

Kutanöz mastositozlar, deride mast hücre infiltrasyonu ile karakterize hastalık grubudur. Deri lezyonlarına iç organ tutulumu da eşlik edebilir. Telenjiektazia makülaris erüptiva perstans, kutanöz mastositozların nadir bir formudur ve genellikle erişkinlerde görülür. Sıklıkla gövdede yuvarlak, oval, kahverengi kırmızı maküler lezyonlar görülür. Olguların üçte birinde sistemik tutulum olabilir. Tedavi, hastalarda sistemik tutulum ve klinik bulguların varlığına göre değişir. 39 yaşındaki erkek hasta gövde ve kollarda yaygın, kahverengi, kaşıntılı maküler lezyonlarla başvurdu. Klinik ve histopatolojik olarak telenjiektazia makülaris erüptiva perstans tanısı konan hastada sistemik tutulum saptanmadı. Telenjiektazia makülaris erüptiva perstans kutanöz mastositozun atipik bir formu olması ve nadir görülmesi nedeniyle olgumuzu sunmayı uygun gördük. Anahtar kelimeler: Kutanöz Mastositoz; Sistemik Tutulum; Telenjiektazia Makülaris Erüptiva Perstans.

Anahtar Kelimeler

Kutanöz Mastositoz; Sistemik Tutulum; Telenjiektazia Makülaris Erüptiva Perstans.

Kaynakça

• Soter NA. The skin in mastocytosis. J Invest Dermatol 1991;96:32–9.
• Soter NA. Mastocytosis and the skin. Hematol Oncol Clin North Am 2000;14:537–55.
• Kalayciyan AK, Kotoğyan A. Telangiectasia macularis eruptiva perstans. J Eur Acad Dermatol Venereol 2001;15:263–4.
• Rishpon A, Matz H, Gat A, Brenner S. Telangiectasia macularis eruptiva perstans: unusual presentation and treatment. Skinmed 2006;5:300–2.
• Sarkany RP, Monk BE, Handfield-Jones SE. Telangiectasia macularis eruptiva perstans: a case report and review of the literature. Clin Exp Dermatol 1998;23:38–9.
• Gibbs NF, Friedlander SF, Harpster EF. Telangiectasia macularis eruptiva perstans. Pediatr Dermatol 2000;17:194– 7.
• Sotiriou E, Apalla Z, Ioannides D. Telangiectasia macularis eruptive perstans successfully treated with PUVA therapy. Photodermatol Photoimmunol Photomed 2010;26:46–7.
• Kökçam İ, Saral Y, Yavrucuoğlu E, Sağlam S, Yılmaz Ş, Uyar B. Telangiectazia macularis eruptiva perstans (urticaria pigmentosa adultorum). T Klin J Dermatol 1997;7:203-7.
• Neri I, Guareschi E, Guerrini V, Patrizi A. Familial telangiectasia macularis eruptiva perstans. Pediatr Dermatol 2005;22:488-9.
• Yıldırım M, Baysal V, Öztürk H, Sarı A. Telenjiektazia Makülaris Erüptiva Perstans: Bir Olgu Sunumu. T Klin Tıp Bilimleri 2002;22:193-5.
• Metcalfe DD. The mastosytosis syndrome. In:.Fitzpatrick TB, Eisen AZ, Wolf K, Freedberg IM, Austton KF, eds. Dermatology in General Medicine. 5th edition. New-york, McGraw-Hill Book Company; 1998. P.1902-7.
• Vidal C, del Rio E, Suárez-Peñaranda J, Armisén M. Telangiectasia macularis eruptiva perstans presented as a pseudoallergic food reaction. J Investig Allergol Clin Immunol 2000;10:248-50.
• Costa DL, Moura HH, Rodrigues R, Pineiro-Maceira J, Ramos-E-Silva M. Telangiectasia macularis eruptiva perstans: a rare form of adult mastocytosis. J Clin Aesthet Dermatol 2011;4:52-4.