Kawasaki disease in adolescence

Öz

Currently a large number of patients are waiting for organ transplantation and newborns with anencephaly are thought to be potential candidates for organ transplantation A male baby was born to a 30 year old mother after 38 weeks of gestation with a birth weight of 2430 g Antenatal ultrasonography performed during the last months of the pregnancy revealed the presence of anencephaly The parents were asked for organ donation from the infant and informed consent was obtained The infant died at the 24th hours of his life Therefore the diagnosis of the brain death which required two clinical examinations and two electroencephalographic examinations with an interval of 48 hours could not be achieved It is not a practical approach in such cases to make a diagnosis of brain death with electroencephalography Therefore new approaches should be developed for anencephalic newborns Ethical and legal issues on this subject are still controversial Here we present the challenges posed by this case and also discuss the difficulty involved in choosing anencephalic neonates as candidate organ donors Turk Arch Ped 2013; 48: 165 8

Anahtar Kelimeler

• Adolescent Kawasaki disease, coronary artery dilatation, pulmonary involvement

Ergenlikte Kawasaki hastalığı

Öz

Kawasaki hastalığı erken çocukluk döneminde görülen koroner arter tutulumu nedeniyle hastalık ve ölüme yol açan bir vaskülittir Büyük çocuk ve ergenlerde nadir görülmesi tanının gecikmesine neden olarak koroner arter tutulumu için bir risk etmeni oluşturabilir Kliniğimizde ergen yaşta Kawasaki hastalığı tanısı koyduğumuz koroner arter genişlemesi ve akciğer tutulumu da gözlenen bir olgumuzu sunuyoruz.

Anahtar Kelimeler

• Akciğer tutulumu
• erişkin Kawasaki hastalığı
• koroner arter genişlemesi

Kaynakça

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