Önceden sağlıklı olan bir çocukta ektima gangrenozum

Öz

Sirenomeli olarak da adlandırılan denizkızı mermaid sendromu oldukça nadir görülen doğumsal bir bozukluktur Bu sendromda bebeğe denizkızı görünümünü veren yapışık bacakların yanı sıra ağır üreme boşaltım mide bağırsak kalp damar ve merkezi sinir sistemi bozuklukları bulunur Bu yazıda yapışık bacakların yanı sıra göbek kordonunda tek arter böbrek yokluğu akciğer hipoplazisi özofagus atrezisi ventriküler septal defekt anal atrezi bağırsak atrezisi saptanan ve doğumunun beşinci saatinde kaybedilen denizkızı sendromu olgusu sunulmuştur.

Anahtar Kelimeler

• Ektima gangrenozum
• Pseudomonas aeruginosa
• Sirenomeli

Ecythema gangrenosum in a previously healthy child

Öz

Ecthyma gangrenosum is a well known cutaneous manifestation of Pseudomonas aeruginosa infections and is usually seen in immunocompromised patients A previously healthy 5 month old boy presented to our hospital with a complaint of an open inguinal wound Physical examination revealed several ulcers surrounded by erythematous halos in bilateral inguinal regions Pseudomonas aeruginosa was isolated from swab cultures obtained from the ulcers However blood cultures were sterile The patient was diagnosed as non bacterial ectima gangrenosoum No immunological abnormality was detected during extensive investigation of the patient The patient was successfully treated with an anti pseudomonal antibiotic cefoperazone sulbactam Turk Arch Ped 2013; 48: 68 70

Anahtar Kelimeler

• Ecthyma gangrenosum, Pseudomonas aeruginosa DO I: 10.4274/tpa.421

Kaynakça

1. Athappan G, Unnikrishnan A, Chandraprakasam S. Ecthyma gangrenosum: presentation in a normal neonate. Dermatol Online J 2008; 14(2):7.
2. Zomorrodi A, Wald ER. Ecthyma gangrenosum: considerations in a previously healthy child. Pediatr Infect Dis J 2002; 21(12): 1161-4.
3. Duman M, Özdemir D, Yiş U, Köroğlu TF, Ören O, Berktaş S. Multiple erythematous nodules and ecthyma gangrenosum as a manifestation of Pseudomonas aeruginosa sepsis in a previously healthy infant. Pediatr Dermatol 2006; 23(3): 243-6.
4. Song WK, Kim YC, Park HJ, Cinn YW. Ecthyma gangrenosum without bacteraemia in a leukaemic patient. Clin Exp Dermatol 2001; 26(5): 395-7. Chan YH, Chong CY, Puthucheary J, Loh TF. Ecthyma gangrenosum: a manifestation of Pseudomonas sepsis in three paediatric patients. Singapore Med J 2006; 47(12): 1080-3.
5. Ishikawa T, Sakurai Y, Tanaka M, et al. Ecthyma gangrenosum-like lesions in a healthy child after infection treated with antibiotics. Pediatr Dermatol 2005; 22(5): 453-6.
6. Morelli JG. Cutaneous bacterial infections. In: Kliegman RM, Behrman RE, Jansen HB, Stanton BF, (ed)s. Nelson textbook of pediatrics. 18th ed. Philadelphia: Saunders, 2007: 2740.
7. Kanehiro A, Nishino M, Yoshioka A, et al. Two case reports of neonatal ecthyma gangrenosum with septicemia. Jpn J Pediatr 1986; 39: 179-84. Altemeier WA, Todd JC, Inge WW. Gram-negative septicemia: a growing threat. Ann Surg 1967; 166(4): 530-42.
8. Huminer D, Siegman-Igra Y, Morduchowicz G, Pitlik SD. Ecthyma gangrenosum without bacteremia. Report of six cases and review of the literature. Arch Intern Med 1987; 147(2): 299-301.

9. Chusid MJ, Hillmann SM. Community-acquired Pseudomonas sepsis in previously healthy infants. Pediatr Infect Dis J 1987; 6(7): 681-4.
10. Mull CC, Scarfone RJ, Conway D. Ecthyma gangrenosum as a manifestation of Pseudomonas sepsis in a previously healthy child. Ann Emerg Med 2000; 36(4): 383-7. Türk Ped Arfl 2013; 48: 68-70 Turk Arch Ped 2013; 48: 68-70 Karbuz ve ark.
11. Ektima gangrenozumlu bir çocuk/ A child with ecythema gangrenosum 70