PFAPA syndrome Invited Editor

Öz

PFAPA syndrome is an autoinflammatory disease of the childhood period presenting with recurrent fever aphthous stomatitis pharyngitis and cervical lymphadenitis The disease is often seen in children under the age of five Fever attacks recur with irregular time intervals and are unresponsive to treatment with antibiotics and antipyretics All of the clinical findings resolve immediately with a single dose of corticosteroid The ultimate treatment method is tonsilloadenoidectomy Main aspects of PFAPA syndrome are mentioned in this review Turk Arch Ped 2009; 44: 80 3 Key words: Aphthous stomatitis periodic fever PFAPA syndrome

Anahtar Kelimeler

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PFAPA sendromu Çağrılı Editör

Öz

PFAPA sendromu çocukluk çağında yineleyen ateş aftöz stomatit farenjit ve servikal adenitle ortaya çıkan bir otoenflamatuar hastalıktır Hastalık çoğunlukla beş yaşın altında ortaya çıkar Hastalığa ait ateş atakları düzensiz aralıklarla yineler ve ortalama 3 4 sürüp kendiliğinden düzelir Ateş çocuklarda genellikle 39 derecenin üzerindedir ve tüm antibiyotik ve ateş düşürücü tedavilere yanıtsızdır Hastalardaki klinik bulguların tümü tek doz kortikosteroid uygulaması ile hemen kaybolur Kalıcı tedavi seçeneği ise çocuklarda uygulanacak olan tonsilloadenoidektomidir Bu derlemede çocukluk çağındaki PFAPA hastalığın özellikleri dile getirilmiştir Türk Ped Arş 2009; 44: 80 3 Anahtar kelimeler: Aftöz stomatit PFAPA sendromu yineleyen ateş

Anahtar Kelimeler

• Aftöz stomatit, PFAPA sendromu, yineleyen ateş

Kaynakça

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