Serial evaluation of bosentan monotherapy in a patient with Eisenmenger syndrome during an 11-year period: A case follow-up report

Öz

Eisenmenger syndrome is a rare disease primarily characterized by severe degrees of irreversible pulmonary arterial hypertension in the setting of congenital heart disease. In this report, we aim to report, on a yearly basis, the clinical, hemodynamic and echocardiographic parameters of a female patient with Eisenmenger syndrome who had been under bosentan treatment during an 11-year follow-up.

Anahtar Kelimeler

• bosentan
• Eisenmenger syndrome
• pulmonary hypertension

Eisenmenger sendromlu bir hastada 11 yıllık dönemde bosentan monoterapisinin seri değerlendirmesi: Olgu takip raporu

Öz

Eisenmenger sendromu, konjenital kalp hastalığı ortamında öncelikle geri dönüşümsüz pulmoner arteriyel hipertansiyon ile karakterize nadir bir hastalıktır. Bu raporda, 11 yıllık bir takip sırasında Bosentan tedavisi altında olan Eisenmenger sendromlu bir kadın hastanın yıllık olarak klinik, hemodinamik ve ekokardiyografik parametrelerini bildirmeyi amaçlıyoruz.

Anahtar Kelimeler

• bosentan
• Eisenmenger sendromu
• pulmoner hipertansiyon

Kaynakça

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