Kısa sürede nükseden overin juvenil tip granüloza hücreli tümörü olan 11 yaşında kız hasta: olgu sunumu

Yıl 2024, Cilt: 24 Sayı: 3, 149 - 152

Oğuz Arslan , Burak Giray , Emin Erhan Dönmez , Doğan Vatansever , Çağatay Taşkıran

Öz

Amaç: Granüloza hücreli over tümörleri tüm malign over tümörlerinin %2-5’ini oluşturur. Seks kord stromal tümörleri arasında görülme sıklığı %90’ın üzerindedir. Granüloza hücreli tümörlerin iki alt tipi vardır; yetişkin tipi (%95) ve juvenil tipi (%5). Bu çalışmada juvenil granüloza hücreli tümörlerin nüksünü göstermeyi amaçladık.
Olgu sunumu: Overin juvenil granüloza hücreli tümörü tanısıyla 11 yaşında evre 1A olmasına rağmen tanısı konulan, postoperatif 14. ayda nüks eden ve sitoredüktif cerrahi yapılan bir olguyu sunduk.
Sonuç: Juvenil granüloza hücreli tümörün erken dönemde prognozu iyi olmakla birlikte; tekrarlama riski nedeniyle yakın takip önemlidir.

Anahtar Kelimeler

Ergenlik, Juvenil granüloza hücreli tümör, Yumurtalık

An 11-year-old girl with juvenile-type granulosa cell tumor of the ovary that recurs in a short time: a case report

Öz

Aim: Ovarian tumors with granulosa cells constitute 2-5% of all malignant ovarian tumors. Its incidence among sex cord stromal tumors is over 90%. There are two subtypes of granulosa cell tumors; adult type (95%) and juvenile type (5%). In this study, we aimed to show the recurrence of juvenile granulosa cell tumors.
Case presentation: We presented a case with a diagnosis of juvenile granulosa cell tumor of the ovary, which was diagnosed at the age of 11, although it was stage 1A, but relapsed at the postoperative 14th month and underwent cytoreductive surgery.
Conclusion: Although juvenile granulosa cell tumor of the prognosis is good in the early stages; it is important to follow up closely due to the risk of recurrence.

Anahtar Kelimeler

Juvenile granulosa cell tumor, Ovary, Puberty

Kaynakça

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