Clinical and Histopathological Features of Renal Angiomyolipomas: Series of 21 Patients

Öz

Angiomyolipoma (AML) of the kidney is a benign tumor that may be misdiagnosed preoperatively as renal cell carcinoma (RCC). This study analyzes patients with renal angiomyolipoma which were diagnosed between 2005-2011. Their clinical and histopathological features were evaluated retrospectively. Demographics of patients, clinical history, clinical diagnosis and pathologic characteristics of the specimen were assessed. 19 of patients were female. Ages ranged from 15 to 68 years. In 13 patients the lesions were discovered incidentally. A single case of tuberous sclerosis (TS) was confirmed in a patient with bilateral lesions. It is important to recognize their characteristic imaging findings and be aware of not mistakenly diagnosed as renal cell carcinoma. Preoperative correct diagnosis is required especially to decide nephron sparing procedures for treatment.

Anahtar Kelimeler

• Angiomyolipoma,Kidney,Prognosis

Renal Anjiomiyolipomaların Klinik ve Histopatolojik Özellikleri: 21 Olguluk Seri

Öz

Renal anjiomiyolipoma, preoperatif olarak renal hücreli karsinoma ile karışabilen böbreğin benign tümörüdür. Çalışmamızda 2005 – 2011 yılları arasında, renal anjiomiyolipoma tanısı almış olgular, retrospektif olarak incelenerek, klinik ve histopatolojik özellikleri ortaya konuldu. Hasta kayıtlarından elde edilen bilgiler, klinik hikâyeleri, klinik tanısı ve cerrahi materyalin histopatolojik özellikleri not edildi. Olguların 19’ u kadındı. Yaş aralığı 15 - 68 arasındaydı. 13 vakada lezyonlar rastlantısal olarak saptandı. Bilateral lezyonu olan bir vakanın tuberosklerozis olduğu belirlendi. Renal anjiomiyolipomaların karakteristik görüntüleme bulgularını ve renal hücreli karsinoma ile karışabileceğini bilmek önemlidir. Özellikle preoperatif olarak bu tümörleri tanımak nefron koruyucu tedavi seçeneklerini değerlendirmek açısından gereklidir.

Anahtar Kelimeler

• Anjiomiyolipoma,Böbrek,Prognoz

Kaynakça

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