Congenital mesoblastic nephroma: case report

Abstract

Aim: Aim of the report is discuss the case who was prenatally diagnosed as congenital mesoblastic nephroma and  postnatal managenent. 

Case: We reported a case of 27 year old gravida 3, parity 1, abortion 1 referred to our clinic with the diagnosis of preterm labour and polihydramniosis at 34. gestational week. The ultrasonografic examination of the patient, with no antenatal follow up before, revealed a fetal biometry of 33 weeks and polyhydramniosis. A 63x66 mm solid mass with reguler border which involves the whole right kidney was determined with ultrasonografic examination of the fetus. Blood flow of the mass was also demonstrated with colour-doppler ultrasound. There was no additional pathology in the other systems and left kidney. The patient was counselled with pediatric nephrology and pediatric surgery departments. Cesarean section was performed with the endication of preterm rupture of membranes and previous history of cesarean section. 2600 gr male baby was delivered. 70x73mm solid mass was confirmed with  neonatal examination of the fetus and nephrectomy was performed on 16th day by pediatric surgery. Pathological examination of the specimen  demonstrated congenital mesoblastic nephroma.

Conclusion: Prenatal care is very important in the diagnosis and treatment of congenital renal masses.

Key Words: Prenatal diagnosis; congenital mesoblastic nephroma; management

Keywords

• Prenatal diagnosis, congenital mesoblastic nephroma, management.

Konjenital mezoblastik nefroma : olgu sunumu

Öz

Amaç: Prenatal tanı almış konjenital mezoblastik nefroma olgusunun sunulması ve yönetiminin tartışılması amaçlanmıştır.

Olgu: 27 yaşında gravida 3, parite 1, abort 1 olan 34.gebelik haftasındaki gebe erken doğum tehditi ve polihidroamniyos tanısı ile nedeniyle kliniğimize refere edilmiştir. Antenatal takipsiz gebenin yapılan ultrason muayenesinde fetal biyometri 33 hafta ile uyumlu olup ve amniyon sıvı miktarı 340 mm polihidramnios olarak tespit edilmiştir. Ayrıca fetüsun değerlendirilmesinde sağ böbrek lojunda 63x66 mm boyutlarında, böbreğide içine alan sınırları düzenli solid kitle tespit edildi. Doppler ultrasonda kitlede kan akımının varlığı gözlendi. Sol böbrek ve diğer sistem muayanelerinde ek patoloji saptanmadı. Hasta pediatrik nefroloji ve çocuk cerrahisi klinikleri tarafından konsülte edildi ve aile durum hakkında bilgilendirildi. Gebenin antenatal takiplerinde, 36. haftada sularının gelmesi ve eski sezeryan olmasından dolayı sezeryan yapılması kararı verildi. Bebeğin yenidoğan kontrolünde 70x73mm boyutlarında olan kitle doğrulanıp; 16. günde çocuk cerrahisi kliniği tarafından nefrektomi operasyonu yapıldı. Patoloji sunucu konjenital mezoblastik nefroma olarak tespit edildi.

Sonuç: Konjenital renal kitlelerin erken tanı ve tedavisinde prenatal tanı önemlidir

Anahtar kelimeler: : Prenatal tanı, konjenital mezoblastik nefroma, yönetim

Anahtar Kelimeler

• Prenatal tanı, konjenital mezoblastik nefroma, yönetim.Congenital Mesoblastic Nephroma: Case Report

Kaynakça

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