A vulvar angiomyofibroblastoma in a child aged girl: first case and literature review

Yıl 2016, , 45 - 47, 08.05.2016

Uğur Keskin Fahri Fıratlıgil , Mustafa Ulubay Ulaş Fidan Müfit Yenen , Ali Ergün

https://doi.org/10.16948/zktb.76647

Öz

Introduction: Angiomyofibroblastoma (AMFB) is a rare seen mesenchymal tumor that is categorized as a genital stromal tumor. It is commonly seen in the middle-aged women usually affecting the vulva and rarely the vagina. A variant called AMFB-like tumors are also rarely seen in male patients. AMFB with its clinical presentation and location can be wrongly diagnosed as an aggressive angiomyxomas, bartholin cyst or lower genital tract lipomas. The treatment of this rare tumor is generally simple surgical excision.

Case - Discussion: In the following case, angiomyofibroblastoma case that was seen in childhood for the first time according to the literature was explained.

Anahtar Kelimeler

angiomyofibroblastoma, child, vulvar

Kız çocuğunda vulvar anjiomyofibroblastoma: en genç olgu ve literatür tarama

Öz

Giriş: Anjiyomyofiblastomlar (AMFB), genital stromal tümörler içerisinde yer alan, nadir izlenen benign mezenkimal tümörlerdir. Çoğunlukla orta yaşlı kadınlarda izlenmekle birlikte, özellikle vulvayı nadiren de vajinayı tutabilmektedir. AMFB benzeri tümörler adı altında, nadiren erkekler de görülebilmektedir. Klinik olarak yerleşim yeri ve klinik prezentasyonu ile bartolin kistleri, alt genital tract lipomları veya nadiren de agresif anjiyomiksomalar ile karışabilmektedir. Bu nadir tümörlerin tedavisi genellikle basit cerrahi eksizyondur.

Olgu - Tartışma: Bu olguda, literatür bilgimize göre çocukluk çağında olan 11 yaşında ki kız çocuğunda ilk kez izlenen AMFB olgusundan bahsedildi.

Anahtar Kelimeler

anjiyomiyofibroblastoma, çocuk, vulva

Kaynakça

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