A neonatal lupus syndrome with pericardial tamponade due to maternal Sjögren’s syndrome

Year 2023, Volume: 48 Issue: 2, 745 - 747, 02.07.2023

Hacer Yapıcıoğlu Mustafa Özdemir Tugay Tepe Tolga Akbaş Ferda Özlü Sevcan Erdem

https://doi.org/10.17826/cumj.1241756

Abstract

Neonatal lupus syndrome (NLS) is a rare disease with dermatological, cardiac, hepatic and hematologic involvement due to placental transfer of anti-Ro/ SSA and anti-La/ SSB antibodies in infants of mothers with autoimmune diseases. Multisystemic involvement is common in infants. Here we present a baby with neonatal lupus syndrome whose mother had Sjögren's syndrome. He presented with thrombocytopenia, then convulsion and cardiac arrest due to pericardial tamponade. So, the risk of NLS should be kept in mind in infants of mothers with autoimmune diseases.

Keywords

Sjögren’s syndrome, Neonatal lupus syndrome, Convulsion, Pericardial tamponade

Maternal Sjögren sendromuna bağlı perikardiyal tamponadı olan neonatal lupus sendromu

Abstract

Neonatal lupus sendromu (NLS), otoimmün hastalığı olan annelerin bebeklerinde anti-Ro/ SSA ve anti-La/ SSB antikorlarının plasental transferine bağlı olarak dermatolojik, kardiyak, hepatik ve hematolojik tutulumla seyreden nadir bir hastalıktır. Bebeklerde multisistemik tutulum sık görülür. Burada, annesinde Sjögren sendromu olan neonatal lupus sendromlu bir olgu sunulmuştur. Bebekte önce trombositopeni, ardından konvülsiyon ve perikardiyal tamponada ikincil kardiyak arrest gelişmiştir. Otoimmün hastalığı olan annelerin bebeklerinde NLS riski akılda tutulmalıdır.

Keywords

Sjögren sendromu, Neonatal lupus sendromu, Konvülziyon, Perikardiyal tamponad

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