The case of syringomyelia accomponied by hidden meningomyelocele in the newborn period

Year 2010, Volume: 41 Issue: 2, 111 - 113, 01.03.2010

Elif Özalkaya Aslı Memişolu Çaktir Didem Arman Tuğba Gürsoy Hüsnü Fahri Ovalı Güner Karatekin

Abstract

The Case Of Syringomyelia AccomponiedBy Hidden Meningomyelocele In The Newborn Period Objective: Syringomyelia is defined as existance of a fluid-filled cavity or syrinx within the spinal cord. Syringomyelia is frequently related with congenital anomaly of spinal cord or craniocervical junction. Case Report: Datas from studies about symptomatic and asymptomatic syringomyelia in newborn period are not adequate yet for this topic. In our case, newborn with sacral mass was hospitalized in newborn intensive care unit. The smooth tissue ultrasonography of sacral area revealed the neural tissue presence. İn our case, the patient suffered from hypotonicity and feeding difficulty and in the physical examination deep tendon reflexes were absent. Since our clinical findings were not corresponding exactly with the finding of hidden syringomyelia, magnetic resonance of lumbosacral area was performed and syringomyelia was detected. Conclusion: As a result, syringomyelia must be considered when clinical findings are not corresponding with anomalies of spinal cord and congenital craniocervical junction.

Keywords

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Yenidoğan döneminde kapalı meniingomiyelosele eşlik eden siringomiyeli vakası

Abstract

Giriş: Siringomiyeli, spinal kordda sıvı dolu kavitenin veya sirinksin genişlemesi olarak tanımlanır. Sıklıkla kranioservikal birleşim ya da sipinal kordun konjenital anormallikleri ile ilişkilidir. Yenidoğanlarda semptomatik veya asemptomatik siringomiyeli için yeterli veri yoktur. Olgu Sunumu: Bu çalışmada sakrumda kitle nedeniyle yenidoğan servisine yatırılan, çekilen yumuşak doku ultrasonu nöral doku ile uyumlu bulunan hasta sunulmuştur. Hastanın klinik izleminde hipotonisite, beslenme güçlüğü saptandı. Fizik bakısında 4 ekstremitede derin tendon refleksleri alınamadı. Klinik bulgularının kapalı meningomiyelosel ile uyumlu olmaması nedeniyle, çekilen lumbosakral manyetik rezonans'ında siringomiyeli saptandı. Sonuç: Çalışmanın amacı konjenital kranioservikal birleşim ve spinal kord anomalliklerinde tanı klinik bulgular ile uyumlu değil ise siringomiyelinin mutlaka düşünülmesi gerektiğini vurgulamaktır.

Keywords

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