A Case Of Ganglioneuroma

Öz

Isolated hamartomatous ganglioneuromas are extremely rare tumors. Although they may be found in adrenal gland or retroperitoneal region most of the time, they are localized in the posterior mediastineum. These hamartomatous tumors may rarely possess malignant foci (areas of neuroblastomaous or malignant nerve sheath tumour). An isolatPd hamartomatous ganglioneuroma in a 17 years old girl localised at upper posterior mediasteneum is presented with its clinical and morphologic characteristics and is discussed with current literature data.

Anahtar Kelimeler

• Ganglioneuroma,VonRecklinghausen's disease,satellite cells

Bir Ganglionoroma Olgusu

Öz

İzole hamartomatoz ganlionöroma son derece nadir tümörlerden biridir. Adrenal bez ve retroperitoneal bölgede izlenmesine karşın en sık arka mediasten yerleşimlidir. Bu hamartomatoz tümörler nadiren malign odaklar (nöroblastomatöz ya da malign sinir kılıfı tümör alanları) içerebilirler. 17 yaşında kız çocukta üst arka mediasten yerleşimli ganglionöroma olgusunun klinik ve morfolojik bulguları sunulmuştur ve son literatürler gözden geçirilerek tartışılmıştır.

Anahtar Kelimeler

• Ganglionöroma,Von Recklinghausen's disease,satellit hücreleri

Kaynakça

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7. Russel DS, Rubinstein LJ. Pathology of Tumours of the Nervous System: Primary Meningeal and Cerebral Sarcomas. London, UK: Butler and Tanner Ltd; 1989.