Tekrarlayan Fasiyal Paralizili bir olgu: Melkersson-Rosenthal Sendromu
Öz
Melkersson-Rosenthal sendromu (MRS), tekrarlayan fasiyal paralizi, orofasiyal ödem, dilde fissürle karakterize nadir bir nöromukokütanöz sendromdur. Oligosemptomatik ve monosemptomatik olgular, klasik triaddan sık görülür. Bulguların ikisinin görülmesi veya bulguların biri ve biyopside granülomatöz keilitin varlığı Melkersson-Rosenthal sendromu tanısı için yeterlidir. Bu yazıda Melkersson-Rosenthal sendromu tanısı alan 12 yaşında bir erkek sunulmuştur.
Anahtar Kelimeler
Melkersson-Rosenthal sendromu, tekrarlayan fasiyal paralizi, çocuklar.
Kaynakça
- Melkersson E. Case of recurrent facial paralysis with angioneurotic edema. Hygiea. 1928;90:737-41.
- Rosenthal C. Klinisch-erbbiologischer Beitrag zur Konstitutions-pathologie: Gemeinsames Auftreten von (rezidivierender familiärer). Facialislähmung, angioneurotischem gesichtsödem und lingua plicata in arthritismus-familien. Ztschr Neurol Psychiatry. 1931;131:475-501.
- Hornstein OP. Melkersson–Rosenthal syndrome: A neuro-mucocutaneous disease of complex origin. Curr Probl Derm. 1973;5:117–56.
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- Rawlings NG, Valenzuela AA, Allen LH, Heathcote JG. Isolated eyelid edema in Melkersson–Rosenthal syndrome: a case series. Eye. 2012;26:163-6.
