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A Rare Case: Sporadic Bladder Paraganglioma

Yıl 2013, Cilt: 38 Sayı: 4, 794 - 799, 01.12.2013

Öz

Paraganglioma is a rare tumor which originates from paraganglia tissue from neural crest. Bladder paraganglioma is suggested to be from crommaffin cells by the remains of the embryological cells. In this report, we aimed to discuss the literature by a case of bladder paraganglioma. A 39 year old male applied to our clinic with gross hematuria. A 2x2 cm mass was revealed in urinary ultrasound. Paraganglioma was found in the resection specimen and partial cystectomy was performed to the patient. A six month follow up revealed no recurrences. Even though bladder paraganglioma is a rare disease, it should be kept in mind for differential diagnosis.

Kaynakça

  • Talbot AR. Paraganglioma of the maxillary sinus. J Laryngol Otol. 1990; 104:248-51.
  • Rodriguez-Cuevas H, Lau I, Rodriguez HP. Highaltitude paragangliomas diagnostic and therapeutic considerations. Cancer. 1986; 57):672-6.
  • Kliewer KE, Wen DR, Cancilla PA, Cochran AJ. Paragangliomas: assessment of prognosis by histologic, immunohistochemical, and ultrastructural techniques. Hum Pathol. 1989; 20:29-39.
  • Lack EE, Cubilla AL, Woodruff JM, Farr HW. Paragangliomas of the head and neck region: a clinical study of 69 patients. Cancer 1977; 39:39740
  • Ueda N, Yoshida A, Fukunishi R, Fujita H, Yanagihara N.Nonchromaffin paraganglioma in the nose and paranasal sinuses.Acta Pathol Jpn. 1985; 35:489-95.
  • Dahm P, Gschwend JE. Malignant Non-urothelial Neoplasms of the Urinary Bladder: A Review. European Urology. 2003; 44:672-81.
  • Das S, Bulusu NV, Lowe P. Primary Vesical Pheochromocytoma. Urology. 1983; 21: 20-5.
  • Ansari MS, Goel A, Goel S, Durairajan LN and Seth A. Malignant Paraganglioma of the Urinary Bladder. A Case Report. International Urology and Nephrology. 2001; 33: 343-5.
  • Pastor-Guzman JM, Lopez-García S, GimenezBachs JM, et al. Paraganglioma of the bladder: controversy regarding treatment. Urol Int. 2004; 73:270-5.
  • Doran F, Varinli S, Bayazit Y, Bal N, Özdemir S. Pheochromocytoma of the urinary bladder. APMIS. 2002; 110:733-6.
  • Zimmerman IJ, Biron RE, MacMahan HE. Pheochromocytoma of the urinary bladder. N Engl J Med. 1953; 249:25-6.
  • Pastor-Guzmán JM, López-García S, GiménezBachs JM, et al. Paraganglioma of the bladder: controversy regarding treatment. Urol Int. 2004; 73:270-5
  • Ansari MS, Goel A, Goel S, Durairajan LN, Seth A. Malignantparaganglioma of the urinary bladder. A case report. Int Urol Nephrol. 2001; 33:343-5.
  • Piedrola G, Lopez E, Rueda MD, Lopez R, Serrano J, SanchoM. Malignant pheochromocytoma of the bladder. Current controversies. Eur Urol. 1997; 31: 122–
  • Neumann HPH, Bausch B, McWhinney SR, et al. Germ-line mutations in nonsyndromic pheochromocytoma. N Engl J Med. 2002; 346:1459
  • Dluhy RG. Pheochromocytoma–death of an axiom. N Engl J Med. 2002; 346:1486-8
  • Kudva YC, Sawka AM, Young WF Jr. The laboratorydiagnosis of adrenal pheochromocytoma: the Mayo Clinic experience. J Clin Endocrinol Metab. 2003; 88:4533-9.
  • Sawka AM, Jaeschke R, Singh RJ, Young WF Jr. A comparison of biochemical tests for pheochromocytoma: measurement of fractionated plasma metanephrines compared with the combination of 24-hour urinary metanephrines and catecholamines. J Clin Endocrinol Metab. 2003; 88: 553–
  • Flanigan RC, Wittmann RP, Huhn RG, and Davis CJ. Malignant pheochromocytoma of the urinary bladder. Urology. 1980; 16: 386–8.
  • Thrasher JB, Rajan RR, Perez LM, Humphrey PA, Anderson EE. Pheochromocytoma of urinary bladder: contemporary methods of diagnosis and treatment options. Urology. 1993; 41: 435-9. Yazışma Adresi / Address for Correspondence: Dr. Hakan Erçil Adana Numune Eğitim ve Araştırma Hastanesi Üroloji Kliniği ADANA e-mail: hakanssk@yahoo.com geliş tarihi/received :01.04.2013 kabul tarihi/accepted:30.04.2013

Nadir Bir Olgu: Sporadik Mesane Paraganglioması

Yıl 2013, Cilt: 38 Sayı: 4, 794 - 799, 01.12.2013

Öz

Paraganglioma nadir olarak görülen ve nöral krest orjinli paraganglia dokusundan gelişen bir tümördür. Mesane paraganglioması, mesane duvarı içinde kromaffin hücrelerin embriyojenik artıklarından kaynaklandığı öne sürülmüştür. Biz bu çalışmamızda mesanede yerleşen primer paraganglioma olgusunu literatür eşliğinde irdeledik. 39 yaşında erkek hasta iki yıldır ağrısız pıhtılı idrar yapma şikayetiyle başvurduğu polikliniğimizde yapılan idrar tahlilinde hematürisi olması üzerine yapılan ultrasonografisinde mesanede 2x2 cmlik kitle saptandı. Patolojisi paraganglioma gelen hastaya parsiyel sistektomi uygulandı. Hastanın 6 aylık takiplerine nüks izlenmedi. Mesane paragangliomasi nadir bir olgu olsa da, mesane tümörü ayırıcı tanısında mutlaka akla getirilmelidir.

Kaynakça

  • Talbot AR. Paraganglioma of the maxillary sinus. J Laryngol Otol. 1990; 104:248-51.
  • Rodriguez-Cuevas H, Lau I, Rodriguez HP. Highaltitude paragangliomas diagnostic and therapeutic considerations. Cancer. 1986; 57):672-6.
  • Kliewer KE, Wen DR, Cancilla PA, Cochran AJ. Paragangliomas: assessment of prognosis by histologic, immunohistochemical, and ultrastructural techniques. Hum Pathol. 1989; 20:29-39.
  • Lack EE, Cubilla AL, Woodruff JM, Farr HW. Paragangliomas of the head and neck region: a clinical study of 69 patients. Cancer 1977; 39:39740
  • Ueda N, Yoshida A, Fukunishi R, Fujita H, Yanagihara N.Nonchromaffin paraganglioma in the nose and paranasal sinuses.Acta Pathol Jpn. 1985; 35:489-95.
  • Dahm P, Gschwend JE. Malignant Non-urothelial Neoplasms of the Urinary Bladder: A Review. European Urology. 2003; 44:672-81.
  • Das S, Bulusu NV, Lowe P. Primary Vesical Pheochromocytoma. Urology. 1983; 21: 20-5.
  • Ansari MS, Goel A, Goel S, Durairajan LN and Seth A. Malignant Paraganglioma of the Urinary Bladder. A Case Report. International Urology and Nephrology. 2001; 33: 343-5.
  • Pastor-Guzman JM, Lopez-García S, GimenezBachs JM, et al. Paraganglioma of the bladder: controversy regarding treatment. Urol Int. 2004; 73:270-5.
  • Doran F, Varinli S, Bayazit Y, Bal N, Özdemir S. Pheochromocytoma of the urinary bladder. APMIS. 2002; 110:733-6.
  • Zimmerman IJ, Biron RE, MacMahan HE. Pheochromocytoma of the urinary bladder. N Engl J Med. 1953; 249:25-6.
  • Pastor-Guzmán JM, López-García S, GiménezBachs JM, et al. Paraganglioma of the bladder: controversy regarding treatment. Urol Int. 2004; 73:270-5
  • Ansari MS, Goel A, Goel S, Durairajan LN, Seth A. Malignantparaganglioma of the urinary bladder. A case report. Int Urol Nephrol. 2001; 33:343-5.
  • Piedrola G, Lopez E, Rueda MD, Lopez R, Serrano J, SanchoM. Malignant pheochromocytoma of the bladder. Current controversies. Eur Urol. 1997; 31: 122–
  • Neumann HPH, Bausch B, McWhinney SR, et al. Germ-line mutations in nonsyndromic pheochromocytoma. N Engl J Med. 2002; 346:1459
  • Dluhy RG. Pheochromocytoma–death of an axiom. N Engl J Med. 2002; 346:1486-8
  • Kudva YC, Sawka AM, Young WF Jr. The laboratorydiagnosis of adrenal pheochromocytoma: the Mayo Clinic experience. J Clin Endocrinol Metab. 2003; 88:4533-9.
  • Sawka AM, Jaeschke R, Singh RJ, Young WF Jr. A comparison of biochemical tests for pheochromocytoma: measurement of fractionated plasma metanephrines compared with the combination of 24-hour urinary metanephrines and catecholamines. J Clin Endocrinol Metab. 2003; 88: 553–
  • Flanigan RC, Wittmann RP, Huhn RG, and Davis CJ. Malignant pheochromocytoma of the urinary bladder. Urology. 1980; 16: 386–8.
  • Thrasher JB, Rajan RR, Perez LM, Humphrey PA, Anderson EE. Pheochromocytoma of urinary bladder: contemporary methods of diagnosis and treatment options. Urology. 1993; 41: 435-9. Yazışma Adresi / Address for Correspondence: Dr. Hakan Erçil Adana Numune Eğitim ve Araştırma Hastanesi Üroloji Kliniği ADANA e-mail: hakanssk@yahoo.com geliş tarihi/received :01.04.2013 kabul tarihi/accepted:30.04.2013
Toplam 20 adet kaynakça vardır.

Ayrıntılar

Birincil Dil Türkçe
Bölüm Araştırma
Yazarlar

Hakan Erçil Bu kişi benim

Umut Ünal Bu kişi benim

Güçlü Gürlen Bu kişi benim

Nevzat Can Şener Bu kişi benim

Tardu Çınar Bu kişi benim

Yalçın Evliyaoğlu Bu kişi benim

Yayımlanma Tarihi 1 Aralık 2013
Yayımlandığı Sayı Yıl 2013 Cilt: 38 Sayı: 4

Kaynak Göster

MLA Erçil, Hakan vd. “Nadir Bir Olgu: Sporadik Mesane Paraganglioması”. Cukurova Medical Journal, c. 38, sy. 4, 2013, ss. 794-9.