BibTex RIS Kaynak Göster

A Tumefactive Multiple Sclerosis Case Mimicking a Focal Cerebral Mass

Yıl 2013, Cilt: 38 Sayı: 2, 329 - 332, 01.06.2013

Öz

Tumefactive multiple sclerosis is a rare demyelinating disease presenting with a focal cerebral mass. Clinically and radiographically, the disease is usually difficult to differentiate from a tumor and abscess. If there is a doubt in the differential diagnosis, visual evoked potentials and CSF analysis and a trial with high dose corticosteroids should contribute to the evaluation of the patient before invasive procedures are started. Here we present a 13 year old girl with left hemiparesis, and a mass lesion on imaging studies confused with a tumor. Gross total tumor excision was performed. The pathology was consistent with a demyelinating disease.

Kaynakça

  • lwamoto K, Oka H, Utsuki S, Ozawa T, Fujii K. Late-onset multiple sclerosis mimicking brain tumor: a case report. Brain Tumor Pathol. 2004; 21:83-6.
  • Renoux C, et al. Natural history of multiple sclerosis with childhood onset. N Enl J Med. 2007; 356:2603-13.
  • Ruggieri M, et al. Multiple sclerosis in children under 10 years of age. Neurol Sci. 2004; 25: 326Compston A, Confavreux C, Lassmann H et al:McAlpine's Multiple Sclerosis, 4. edition, Churchill Livingstone, China. 2006. Brunot E, Marcus JC. Multiple Sclerosis presenting as a single mass lesion. Pediatr Neurol. 1999; 20:383-6.
  • Chabas D, Gren AJ, Waubant E. Pediatric multiple sclerosis. The American Society for Experimental NeuroTherapeutics. 2006; 3:264–75.
  • Köksal V, Ekici MA, Menkü A, Bulut T, Öktem İS. Serebral tümörle karışan iki multiple skleroz olgusu. Erciyes Tıp Dergisi (Erciyes Medical Journal). 2008; 30:111-6.
  • Nilsson P. Hemicraniectomy in tumefactive demyelinating disease. European Neurological Journal; 2010; 1-9.
  • Prockop LD, Heinz ER. Demyelinating disease presenting as an intracranial mass lesion. Arch Neurol. 1965; 13:559-64.
  • Van der Velden M, Bots GT, Endtz LJ. Cranial CT in multiple sclerosisshwing a mass effect. Surg Neurol. 1979; 12:307–10.
  • Giang DW, Poduri KR, Eskin TA, et al. Multiple sclerosis masquerading as a mass lesion Neuroradiology. 1992; 34:150–4.
  • Yapici Z, Eraksoy M. Bilateral demyelinating tumefactive lesions in three children with hemiparesis. J Child Neurol. 2002;1 7:655–60.

İntrakraniyal Kitleyi Taklit Eden Tumefaktif Multipl Skleroz Olgusu

Yıl 2013, Cilt: 38 Sayı: 2, 329 - 332, 01.06.2013

Öz

Tümefaktif multiple skleroz fokal serebral kitle olarak prezante olan nadir bir demiyelinizan hastalıktır. Klinik ve radyolojik olarak genellikle tümör veya apseden ayrımı zordur. Ayırıcı tanıda eğer şüphe varsa invazif girişimlerden önce görsel uyarılmış potansiyeller ve BOS analizi yapılması, yüksek doz kortikosteroid tedavisi denenmesi önerilmektedir. Bu yazıda sol hemiparezi ile başvuran, radyolojik olarak lezyonu kitle lezyonu olarak değerlendirilip gross total tümör eksizyonu uygulanmış ancak patoloji sonucu demiyelinizan hastalık ile uyumlu gelen 13 yaşında bir kız hasta sunulmuştur. Tümefaktif multipl skleroz, multipl skleroz, fokal serebral lezyon

Kaynakça

  • lwamoto K, Oka H, Utsuki S, Ozawa T, Fujii K. Late-onset multiple sclerosis mimicking brain tumor: a case report. Brain Tumor Pathol. 2004; 21:83-6.
  • Renoux C, et al. Natural history of multiple sclerosis with childhood onset. N Enl J Med. 2007; 356:2603-13.
  • Ruggieri M, et al. Multiple sclerosis in children under 10 years of age. Neurol Sci. 2004; 25: 326Compston A, Confavreux C, Lassmann H et al:McAlpine's Multiple Sclerosis, 4. edition, Churchill Livingstone, China. 2006. Brunot E, Marcus JC. Multiple Sclerosis presenting as a single mass lesion. Pediatr Neurol. 1999; 20:383-6.
  • Chabas D, Gren AJ, Waubant E. Pediatric multiple sclerosis. The American Society for Experimental NeuroTherapeutics. 2006; 3:264–75.
  • Köksal V, Ekici MA, Menkü A, Bulut T, Öktem İS. Serebral tümörle karışan iki multiple skleroz olgusu. Erciyes Tıp Dergisi (Erciyes Medical Journal). 2008; 30:111-6.
  • Nilsson P. Hemicraniectomy in tumefactive demyelinating disease. European Neurological Journal; 2010; 1-9.
  • Prockop LD, Heinz ER. Demyelinating disease presenting as an intracranial mass lesion. Arch Neurol. 1965; 13:559-64.
  • Van der Velden M, Bots GT, Endtz LJ. Cranial CT in multiple sclerosisshwing a mass effect. Surg Neurol. 1979; 12:307–10.
  • Giang DW, Poduri KR, Eskin TA, et al. Multiple sclerosis masquerading as a mass lesion Neuroradiology. 1992; 34:150–4.
  • Yapici Z, Eraksoy M. Bilateral demyelinating tumefactive lesions in three children with hemiparesis. J Child Neurol. 2002;1 7:655–60.
Toplam 10 adet kaynakça vardır.

Ayrıntılar

Birincil Dil Türkçe
Bölüm Araştırma
Yazarlar

Olcay Ünver Bu kişi benim

Zehra İşık Hasıloğlu Bu kişi benim

Umut Durak Bu kişi benim

Serap Uysal Bu kişi benim

Yayımlanma Tarihi 1 Haziran 2013
Yayımlandığı Sayı Yıl 2013 Cilt: 38 Sayı: 2

Kaynak Göster

MLA Ünver, Olcay vd. “İntrakraniyal Kitleyi Taklit Eden Tumefaktif Multipl Skleroz Olgusu”. Cukurova Medical Journal, c. 38, sy. 2, 2013, ss. 329-32.