A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report

Şebnem Kader; Pınar Gökçe Reis; Mehmet Mutlu; Yakup Aslan; Erol Erduran; Uğur Yazar

doi:10.5798/dicletip.339025

A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report

Öz

Intracranial hemorrhage among term newborns is a rare clinical condition with high morbidity and mortality. Although major bleeding is relatively uncommon, the incidence of intracranial hemorrhage in hemophilic children is higher during the first few days of life than at any other stage in childhood, which relates to the trauma of delive ry.

Here, we reported a newborn case diagnosed with moderate hemophilia A, without the presence of a positive family

history of hemophilia and presenting with intracranial and extracranial hemorrhage and we aimed to emphasize that the early diagnosis and replacement therapy carries an essential importance.

Anahtar Kelimeler

newborn,hemophilia A,intracranial hemorrhage

Kaynakça

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4. Kulkarni R, Lusher JM. Intracranial and extracranial hemorrhages in newborns with hemophilia: a review of the literature. J Pediatr Hematol Oncol.1999;21:289-95.
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6. Byams VR, Kouides PA, Kulkarni R, et al. Surveillance of female patients with inherited bleeding disorders in United States Haemophilia Treatment Centres. Haemophilia. 2011;17:6-13.
7. Walker I, Pai M, Akabutu J, et al. The Canadian Hemophilia Registry as the basis for a national system for monitoring the use of factor concentrates. Transfusion. 1995; 35:548-51.
8. Geraghty S, Dunkley T, Harrington C, et al. Practice patterns in haemophilia A therapy -global progress towards optimal care. Haemophilia. 2006; 12:75-81.

9. White GC, 2nd, Rosendaal F, et al. Definitions in hemophilia. Recommendation of the scientific subcommittee on factor VIII and factor IX of the scientific and standardization committee of the International Society on Thrombosis and Haemostasis. Thromb Haemost. 2001; 85:560. 10. Chadwick LM, Pemberton PJ, Kurinczuk JJ. Neonatal subgaleal haematoma: associated risk factors, complications and outcome. J Paediatr Child Health.1996; 32:228-32.
11. Le Pommelet C, Durand P, Laurian Y, Devictor D. Haemophilia A: two cases showing unusual features at birth. Haemophilia. 1998;4: 122-5.
12. Johnson-Robbins LA, Porter JC, Horgan MJ. Splenic rupture in a newborn with hemophilia A: case report and review of the literature. Clin Pediatr. 1999; 38:117-9.
13. Plauche WC. Subgaleal hematoma. A complication of instrumental delivery. JAMA. 1980; 244:1597-8.
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18. Baehner RL, Strauss HS. Hemophilia in the first year of life. N Engl J Med.1966; 275:524-8.
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Ayrıntılar

Birincil Dil

İngilizce

Konular

-

Bölüm

Olgu Sunumu

Yazarlar

Şebnem Kader Bu kişi benim
0000-0001-7585-4228
Türkiye

Pınar Gökçe Reis Bu kişi benim
0000-0001-9684-3595
Türkiye

Mehmet Mutlu Bu kişi benim
0000-0003-3666-3159
Türkiye

Yakup Aslan Bu kişi benim
0000-0001-9668-9559
Türkiye

Erol Erduran Bu kişi benim
Türkiye

Uğur Yazar Bu kişi benim
Türkiye

Yayımlanma Tarihi

20 Eylül 2017

Gönderilme Tarihi

20 Eylül 2017

Kabul Tarihi

-

Yayımlandığı Sayı

Yıl 2017 Cilt: 44 Sayı: 3

DOI

https://doi.org/10.5798/dicletip.339025

IZ

https://izlik.org/JA58US73AB

Kaynak Göster

RIS / Bibtex

APA

Kader, Ş., Reis, P. G., Mutlu, M., Aslan, Y., Erduran, E., & Yazar, U. (2017). A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report. Dicle Medical Journal, 44(3), 293-298. https://doi.org/10.5798/dicletip.339025

AMA

1.Kader Ş, Reis PG, Mutlu M, Aslan Y, Erduran E, Yazar U. A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report. diclemedj. 2017;44(3):293-298. doi:10.5798/dicletip.339025

Chicago

Kader, Şebnem, Pınar Gökçe Reis, Mehmet Mutlu, Yakup Aslan, Erol Erduran, ve Uğur Yazar. 2017. “A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report”. Dicle Medical Journal 44 (3): 293-98. https://doi.org/10.5798/dicletip.339025.

EndNote

Kader Ş, Reis PG, Mutlu M, Aslan Y, Erduran E, Yazar U (01 Eylül 2017) A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report. Dicle Medical Journal 44 3 293–298.

IEEE

[1]Ş. Kader, P. G. Reis, M. Mutlu, Y. Aslan, E. Erduran, ve U. Yazar, “A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report”, diclemedj, c. 44, sy 3, ss. 293–298, Eyl. 2017, doi: 10.5798/dicletip.339025.

ISNAD

Kader, Şebnem - Reis, Pınar Gökçe - Mutlu, Mehmet - Aslan, Yakup - Erduran, Erol - Yazar, Uğur. “A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report”. Dicle Medical Journal 44/3 (01 Eylül 2017): 293-298. https://doi.org/10.5798/dicletip.339025.

JAMA

1.Kader Ş, Reis PG, Mutlu M, Aslan Y, Erduran E, Yazar U. A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report. diclemedj. 2017;44:293–298.

MLA

Kader, Şebnem, vd. “A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report”. Dicle Medical Journal, c. 44, sy 3, Eylül 2017, ss. 293-8, doi:10.5798/dicletip.339025.

Vancouver

1.Şebnem Kader, Pınar Gökçe Reis, Mehmet Mutlu, Yakup Aslan, Erol Erduran, Uğur Yazar. A newborn with moderate hemophilia A with severe intracranial and extracranial hemorrhage: A case report. diclemedj. 01 Eylül 2017;44(3):293-8. doi:10.5798/dicletip.339025

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