Primer Plazma Hücreli Lösemi: Olgu Sunumu

Yıl 2019, Cilt: 46 Sayı: 2, 393 - 396, 11.06.2019

Sinan Demircioğlu Ali Doğan Murat Altınbaşak Cengiz Demir

https://doi.org/10.5798/dicletip.575025

Öz

Plazma hücreli lösemi (PHL), plazma hücreli diskrazilerin nadir görülen bir formudur. Primer ve sekonder PHL olmak üzere iki formu vardır. Prognozu oldukça kötüdür. Morfolojik olarak matür plazma hücrelerine benzememesi sebebiyle tanıda karışıklıklar olabilmektedir. Tedavide bortezomib bazlı rejimler ve otolog kök hücre nakli önerilmektedir. 

Anahtar Kelimeler

Morfoloji, multiple myelom, plazma hücreli lösemi

Kaynakça

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