Prenatally Diagnosed Vein Of Galen Aneurysm Presenting With Cardiac Failure

Öz

Vein of Galen aneurysm is a rare congenital anomaly, originated from a defect in fusion of internal cerebral veins. It constitutes 1% of all intracranial vascular malformations. Due to low resistance, it produces high-output cardiac failure 1,2 . A 39-year-old woman was diagnosed Galen vein aneurysmal malformation with the ultrasonographic finding of dilated structure in the midline of the brain and turbulent flow within the dilated vascular structure showed with color flow Doppler ultrasonography at the 26th gestational week. We report the subject diagnosed prenatally in our clinic in light of the literature.

Anahtar Kelimeler

• Vein of Galen aneurysm,prenatal diagnosis,cardiac failure

Kardiyak Yetmezlikle Başvuran Galen Ven Anevrizmasının Prenatal Tanısı

Öz

Galen ven anevrizması, internal serebral venlerin füzyon defektinden kaynaklanan nadir bir konjenital anomalidir. İntrakraniyal vasküler malformasyonların %1’ini oluşturur. Düşük direnç nedeniyle, yüksek debili kardiyak yetmezlik yapar 1,2 . 39 yaşındaki olguya, ultrasonografide beyin orta hattında genişlemiş yapı ve renkli akım Dopler ultrasonografide bu yapı içinde türbülan akım izlenmesi ile 26. gebelik haftasında Galen ven anevrizması tanısı konuldu. Kliniğimizde prenatal tanısı konulan bu olgu literatür bilgileri ışığında sunulmaktadır.

Anahtar Kelimeler

• Galen ven anevrizması,prenatal tanı,kardiyak yetmezlik

Kaynakça

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