SKALPTE ATİPİK FİBROKSANTOM OLGUSU

Öz

Atipik fibroksantom nadir görülen, düşük dereceli bir neoplazm olup, sıklıkla güneşe maruz kalan yaşlı hastalarda görülmektedir. Fibroblastlardan kaynaklanan bu hastalığın tanısında klinik, histopatolojik ve immünokimyasal özelliklerinin incelenmesi ve böylece karsinom, melanom, malign fibröz histiyositom gibi malign bazı tanılardan ayrılması gerekmektedir. Olguların büyük çoğunluğu benign olup metastaza nadir olarak rastlanmaktadır. Çalışmamızda 75 yaşında bir erkek hastada 1,5 ay önce parietal alanda ortaya çıkan, başvuru sırasında palpasyonla sert üzeri hafif kanamalı ağrısız nodüler lezyon ile prezente olan atipik fibroksantom olgusu klinik ve patolojik bulgular eşliğinde sunulmuştur. Olgunun metastatik lezyonu, lenfovasküler veya derin invazyonu bulunmamaktadır. Tartışma bölümünde vaka ayırıcı tanı açısından diğer bir takım hastalıklarla histopatolojik ve immünokimyasal olarak karşılaştırılmıştır. Son olarak seçilen cerrahi tedavi yöntemin yeterliliği değerlendirilmiştir.

Anahtar Kelimeler

• Atipik fibroksantom,skalp,düşük dereceli neoplazi

ATYPICAL FIBROXANTHOMA IN SCALP

Öz

Atypical fibroxanthoma is an uncommon neoplasm generally found in elderly patients on sun-exposed areas. Both clinical, histopathological and immunohistochemical features of this fibroblastic process should be assessed in order to be able to diagnose and differentiate it from a number of malignant entities such as carcinoma, melanoma and malignant fibrous histiocytoma. The majority of cases of atypical fibroxanthoma are benign, and metastasis is a rare phenomenon. In this report a 75 year old male patient complaining of a parietally located, painless, mildly hemorrhagic, hard nodular lesion for 1,5 month diagnosed as atypical fibroxanthoma is presented with its clinical and histopathological findings. There was no metastatic lesion, lymphovascular and deep invasion areas microscopically. In the discussion part, the diagnosis was compared with some other entities in histopathological and immunohistochemical manner with regard to differential diagnosis. Lastly the adequacy of the chosen surgical method for the case is discussed and commented.

Anahtar Kelimeler

• Atypical fibroxanthoma,scalp,low grade neoplasia

Kaynakça

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