İNSİDENTAL SAPTANAN MEZENTERİK KALSİFİYE FİBRÖZ TÜMÖR: OLGU SUNUMU

Öz

Kalsifiye fibröz tümör, nadir görülen iğsi hücreli bir tümördür. Genelikle insidental olarak saptanır, fakat semptomatik olduğunda tutulum bölgesine göre klinik prezentasyon farklılık gösterir. İntra abdominal bölge, yumuşak doku ve plevra predileksiyonu gösterir. Sıklıkla çocuk ve genç erişkinlerde izlenir. Hücreden fakir fibrokollagenöz stroma zemini, lenfoplazmositik agregatlar ve lenfoid foliküller, distrofik ve/veya psammomatöz kalsifikasyon içeren spesifik histopatolojik özelliklere sahiptir. Az sayıdaki iğsi hücrelerde vimentin ve faktör XIIIa pozitivitesi saptanır. Biz burada insidental olarak saptanan mezenterik kalsifiye fibröz tümör vakasını benign ve malign lezyonlarla klinikopatolojik olarak karışabilmesi, nadir görüldüğü için akla gelmesi zor bir antite olması sebebiyle, literatür bilgisi eşliğinde sunmayı amaçladık.

Anahtar Kelimeler

• Psödotümör
• kalsifiye
• mezenterik

Incidental Calcifying Fibrous Tumor: A Case Report

Öz

Calcifying fibrous tumor is a rare spindle cell tumor. Despite the fact that it is usually detected incidentally, clinical presentation differs according to the region of involvement when it is symptomatic. Calcifying fibrous tumor shows intra-abdominal region, soft tissue and pleural predilection and is frequently seen in children and young adults. It has specific histopathological features, including paucicellular fibrocollagenous stroma, lymphoplasmocytic aggregates and lymphoid follicles, dystrophic and / or psammomatous calcification. Few spindle cells in pauci cellular stroma are immunoreactive for Vimentin and Factor XIIIa. Here in, we aimed to present the case of incidental mesenteric calcifying fibrous tumor with a literature review, as it is a rare entity and can mimic benign and malignant lesions clinicopathologically.

Anahtar Kelimeler

• Pseudotumor
• calcifying
• mesenteric

Kaynakça

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