Plexiform Myxoid Gastrointestinal Stromal Tumor, A Rare Histological Pattern Located in the Small Intestine: A Case Report

Yıl 2022, Cilt: 44 Sayı: 1, 129 - 133, 14.01.2022

Leymune Parlak , Rabia Altunbaş Erdem Özdemir Emine Zeynep Tarini , Buket Gedik

https://doi.org/10.20515/otd.913177

Öz

Gastrointestinal stromal tumor (GIST) is the most common mesenchymal tumor of the gastrointestinal system originating from kajal cells. It is frequently seen after the age of 50 and 60% in the stomach, the second most frequently in the jejunum and ileum (30%). Small bowel residents have 40-50% more malignant prognosis than those in the stomach. In addition, small intestine GISTs do not constitute distinctive histological subtypes like gastric GISTs. They are mostly spindle cell. Epithelioids, on the other hand, constitute a very small part. In our case, in addition to epithelioid and spindle cell features, there is a plexiform growth pattern and myxoid stroma in the ground.

Anahtar Kelimeler

GIST, Small bowel, Plexiform, Myxoid

Pleksiform Miksoid Gastrointestinal Stromal Tümör, İnce Barsak Yerleşimli Nadir Bir Histolojik Patern: Olgu Sunumu

Öz

Gastrointestinal stromal tümör (GİST) gastrointestinal sistemin en sık görülen, kajal hücrelerinden köken alan mezenkimal tümörüdür. Sıklıkla 50 yaş sonrası ve %60 oranında midede, ikinci sıklıkla jejunum ve ileumda (%30) görülür. İnce barsak yerleşimliler midede bulunanlara göre %40-50 daha fazla malign seyirlidir. Ayrıca ince bağırsak GISTleri mide GISTleri gibi ayırt edici histolojik alt tipler oluşturmazlar. Çoğunlukla iğsi hücrelidirler. Epiteloidler ise çok küçük bir kısmını oluşturur. Bizim sunacağımız olguda epiteloid ve iğsi hücre özelliklerine ek olarak pleksiform büyüme paterni ve zeminde miksoid stroma bulunmaktadır.

Anahtar Kelimeler

GİST, İnce barsak, Pleksiform, Miksoid

Kaynakça

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