LIGNEOUS CONJUNCTIVITIS IN A DANDY-WALKER SYNDROME: A RARE CASE

Öz

Ligneous conjunctivitis is a disease usually characterized by type 1 plasminogen deficiency. As well as being inherited, it may also be associated with infection or trauma. It is characterized by the woody appearance of pseudo-membranes rich in fibrin, especially seen in the tarsal conjunctiva. İn its treatment heparin, alpha chymotrypsin, topical hyaluronidase, corticosteroids, cyclosporine, and surgical excision of membranes exist. In this study, we aimed to demonstrate the association of hydrocephalus and ligneous conjunctivitis in a 10-month-old male patient who had a ventricular-peritoneal shunt for hydrocephalus.

Anahtar Kelimeler

• Ligneous conjunctivitis
• Hydrocephalus
• Dandy–Walker sydrome

YENİ DOĞANDA GÖRÜLEN LİGNÖZ KONJOKTİVİT VE DANDY-WALKER SENDROMU İLİŞKİSİ: NADİR BİR OLGU

Öz

Lignöz konjoktivit, genellikle tip 1 plazminojen eksikliği ile karakterize bir hastalıktır. Genetik kalıtımlı olduğu gibi enfeksiyon veya travma ile de ilişkili olabilir. Özellikle tarsal konjonktivada görülen odunsu görünümde fibrinden zengin psödomembranlarla karakterizedir. Tedavisinde; heparin, alfa kimotripsin, topikal hiyalüronidaz, kortikosteroidler, siklosporin ve membranların cerrahi eksizyonu yer almaktadır. Bu çalışmada, hidrosefali nedeniyle ventrikülo-peritoneal şant uygulanmış 10 aylık erkek hastada Dandy- Walker spektrumuna bağlı hidrosefali ve lignöz konjonktivit birlikteliğini göstermek amaçlanmıştır.

Anahtar Kelimeler

• Lignöz Konjoktivit
• Hidrosefali
• Dandy-Walker Sendromu

Kaynakça

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