Geç Başlangıçlı Lineer Skleroderma

Öz

En coup de sabre (yüzün lineer skleroderması), alın ve saçlı derinin frontopariyetal bölgesini tutan, morfeanın (lineer skleroderma) nadir görülen bir tipidir. Gelişiminde travma, immobilizasyon, BCG aşısı, K vitamini enjeksiyonları, giysilerin mekanik basısı gibi tetikleyiciler suçlanmıştır. En coup de sabre genellikle pediatrik popülasyonda görülür, olguların %67’si 18 yaşından önce tanı almıştır. Burada, 30 yaşında yetişkin bir hastaki en coup de sabre geç başlangıcı vurgulamak amacıyla sunulmuştur.

Anahtar Kelimeler

• En coup de sabre,lokalize skleroderma,morfea,geç başlangıç

Late Onset Linear Sclorederma

Öz

En coup de sabre (linear scleroderma of face) is a rare type of morphea (localized scleroderma) involving frontoparietal area of the forehead and scalp. Many triggering factors have been blamed in the development of morfea like trauma, immobilization, BCG vaccination, injections of vitamin K, mechanical compression from clothing, etc. En coup de sabre usually affects the pediatric population, with 67 % of patients diagnosed before 18 years of age. In this article, it was reported to emphasize the late started a case of 30 years old female.

En coup de sabre (yüzün lineer skleroderması), alın ve saçlı derinin frontopariyetal bölgesini tutan, morfeanın (lineer skleroderma) nadir görülen bir tipidir. Gelişiminde travma, immobilizasyon, BCG aşısı, K vitamini enjeksiyonları, giysilerin mekanik basısı gibi tetikleyiciler suçlanmıştır. En coup de sabre genellikle pediatrik popülasyonda görülür, olguların %67’si 18 yaşından önce tanı almıştır. Burada, 30 yaşında yetişkin bir hastaki en coup de sabre geç başlangıcı vurgulamak amacıyla sunulmuştur.

Anahtar Kelimeler

• En coup de sabre,localized scleroderma,morphea

Kaynakça

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