Geç Başlangıçlı Lineer Skleroderma

Yıl 2018, Cilt: 12 Sayı: 2, 153 - 155, 29.06.2018

İsmet Sevimli Perihan Öztürk , Mehmet Kamil Mülayım , Hülya Nazik

https://doi.org/10.21763/tjfmpc.432556

Cited By: 1

Öz

En coup de sabre (yüzün lineer skleroderması), alın ve saçlı derinin frontopariyetal bölgesini tutan, morfeanın (lineer skleroderma) nadir görülen bir tipidir. Gelişiminde travma, immobilizasyon, BCG aşısı, K vitamini enjeksiyonları, giysilerin mekanik basısı gibi tetikleyiciler suçlanmıştır. En coup de sabre genellikle pediatrik popülasyonda görülür, olguların %67’si 18 yaşından önce tanı almıştır. Burada, 30 yaşında yetişkin bir hastaki en coup de sabre geç başlangıcı vurgulamak amacıyla sunulmuştur.

Anahtar Kelimeler

En coup de sabre, lokalize skleroderma, morfea, geç başlangıç

Late Onset Linear Sclorederma

Öz

En coup de sabre (linear scleroderma of
face) is a rare type of morphea (localized scleroderma) involving frontoparietal
area of the forehead and scalp. Many triggering factors have been blamed in the
development of morfea like trauma, immobilization, BCG vaccination, injections
of vitamin K, mechanical compression from clothing, etc. En coup de sabre
usually affects the pediatric population, with 67 % of patients diagnosed
before 18 years of age. In this article, it was reported to emphasize the late
started a case of 30 years old female.

En coup de sabre (yüzün lineer skleroderması), alın ve saçlı
derinin frontopariyetal bölgesini tutan, morfeanın (lineer skleroderma) nadir
görülen bir tipidir. Gelişiminde travma, immobilizasyon, BCG aşısı, K vitamini
enjeksiyonları, giysilerin mekanik basısı gibi tetikleyiciler suçlanmıştır. En
coup de sabre genellikle pediatrik popülasyonda görülür, olguların %67’si 18
yaşından önce tanı almıştır. Burada, 30 yaşında yetişkin bir hastaki en coup de
sabre geç başlangıcı vurgulamak amacıyla sunulmuştur.

Anahtar Kelimeler

En coup de sabre, localized scleroderma, morphea

Kaynakça

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