Kikuchi Fujimoto disease associated with hemophagocytic syndrome

Öz

Kikuchi Fujimoto disease is a rare condition during childhood characterized with fever and cervical lymphadenopathy Definitive diagnosis of the disease can only be made histologically on lymph node biopsy Hemophagocytic syndrome associated with Kikuchi Fujimoto disease is especially rare In this article we present a case of an eight years old girl diagnosed as hemophagocytic syndrome associated with Kikuchi Fujimoto disease Turk Arch Ped 2013; 48: 71 3

Anahtar Kelimeler

• Hemophagocytic syndrome, Kikuchi-Fujimoto disease, lymphadenopathy,

Kikuchi Fujimoto hastalığı ile birlikte hemofagositik sendrom

Öz

Kikuchi Fujimoto hastalığı ateş ve boyunda lenfadenopati ile nitelenen çocukluk çağında nadir görülen bir hastalıktır Hastalığın kesin tanısı sadece histolojik olarak lenf nodu biyopsi ile konulabilir Kikuchi Fujimoto hastalığının hemofagositik sendromla birlikteliği çok daha nadirdir Bu makalede Kikuchi Fujimoto hastalığıyla birlikte hemofagositik sendrom tanısı alan sekiz yaşındaki kız olgu sunulmuştur.

Anahtar Kelimeler

• Hemofagositik sendrom
• Kikuchi-Fujimoto hastalığı
• lenfadenopati

Kaynakça

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14. Kikuchi-Fujimoto hastalığı ile birlikte hemofagositik sendrom / Kikuchi-Fujimoto disease associated hemophagocytic syndrome Türk Ped Arfl 2013; 48: 71-3 Turk Arch Ped 2013; 48: 71-3