Collet-sicard sendromu ile gelen glomus jugulare olgusu

Öz

Collet-Sicard sendromu (CSS), jugular foramen ve hipoglossal kanal bölgesini etkileyen kafa tabanı lezyonlarında görülen tek taraflı 9 ,10, 11 ve 12. kraniyal sinirlerin paralizisidir. Amacımız kliniğimizde tanı alan CSS vakasını literatür bilgileri eşliğinde sunmaktır. 68 yaş kadın hasta polikliniğe 2 senedir devam eden sağ kulakta çınlama şikayetiyle başvurdu. Sağ timpanik membranda kırmızı-mor renkli refle görüldü. Dil sağ yarısında atrofi, video laringoskopide sağ vokal kord paralitik izlendi. Sağ omuz ve trapezius kası sola göre deprese görünümdeydi. Hastaya Gamma Knife radyocerrahi tedavisi planlandı. 1. yıl kontrol görüntülemede tümör progresyonu saptanmadı. Hastanın klinik bulgularında belirgin iyileşme gözlenmedi. Collet-Sicard sendromuyla gelen glomus tümörleri nadirdir. Nadir görülmesi sebebi ile etkin bir tedavi kılavuzu bulunmamaktadır. Prognoz hakkında bilgiler yetersizdir. Daha kapsamlı vaka serilerinin olduğu randomize kontrollü çalışmalara ihtiyaç bulunmaktadır.

Anahtar Kelimeler

• COLLET-SİCARD SENDROMU
• GLOMUS JUGULARE TÜMÖRÜ
• KRANİYAL SİNİR PARALİZİSİ
• KAFA TABANI LEZYONU

A case of glomus jugulare presentıng wıth collet-sıcard syndrome

Öz

Collet-Sicard Syndrome (CSS) is a unilateral paralysis of the 9th, 10th, 11th, and 12th cranial nerves, seen in skull base lesions affecting the jugular foramen and hypoglossal canal regions. Our aim is to present a case of CSS diagnosed in our clinic, accompanied by relevant literature. A 68-year-old female patient presented to the outpatient clinic with complaints of tinnitus in the right ear, ongoing for two years. Otoscopic examination revealed a reddish-purple reflex on the right tympanic membrane. Atrophy was observed on the right side of the tongue, and videolaryngoscopy showed right vocal cord paralysis. The right shoulder and trapezius muscle appeared depressed compared to the left. Gamma Knife radiosurgery was planned for the patient. At the 1-year follow-up imaging, no tumor progression was detected. However, no significant clinical improvement was observed. Glomus tumors presenting with Collet-Sicard syndrome are rare. Due to its rarity, there is no established treatment guideline. Information regarding prognosis is limited. There is a need for randomized controlled studies with more comprehensive case series.

Anahtar Kelimeler

• COLLET-SICARD SYNDROME
• GLOMUS JUGULARE TUMOR
• CRANIAL NERVE PARALYSIS
• SKULL BASE LESIONS

Kaynakça

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