Primer amenore: Olgu serileri

Öz

Primer amenore, üreme çağındaki kadınların %0.1 ile %2.5'nda görülmektedir. Başlıca nedenleri gonadal yetmezlik (%48.5), uterus ve vajinanın konjenital yokluğu (%16.2) ve konstitüsyonel gecikme (% 0.5) 'dir. Adet göremeyen hastaların, hikayesi ve fizik muayenesi çok önemlidir ve bunun yanında TSH, prolaktin, FSH, LH ve estradiol hormon seviyeleri ve karyotip analizi de gerekebilir. Ultrason (US) ve magnetik rezonans görüntüleme (MRG), görüntüleme yöntemleri arasındadır. Eğer klinik ve US veya MRG arasında farklılıklar var ise tanıyı konfirme etmek için laparoskopi yapılabilir. Burada primer amenore ile polikliniğimize başvuran 3 olguyu sunmak istedik. Bu olgulara yukarıda vurguladığımız yöntemler sayesinde Turner sendromu (TS), Mayer Rokitansky Küs ter Hauser sendromu (MRKH) ve hipogonadotropik hipogonadizm ?(HH) tanıları konmuştur.

Anahtar Kelimeler

• Amenore,Turner sendromu,Genç erişkin,Kadın,Hipogonadizm

Primer amenore: Olgu serileri

Öz

Primary amenorrhea occurs in 0.1% to %2.5% of women in the reproductive age group. Gonadal deficiency (%48.5), congenital agenesis of uterus and vagina (%16.2) and constitutional delay (% 0.5) are the major reasons. Medical history and physical examination are very important in patients who are amenorrheic and besides TSH, prolactin, FSH, LH and estradiol hormone levels and karyotype analysis also may be needed. Ultrasound (US) and magnetic resonans imaging (MRI) are among the imaging procedures. If there is discrepancies between clinical signs and US or MRI findings, laparoscopy can be performed for confirmation of diagnosis. Here, we would like to report 3 cases who were admitted to our outpatient clinic with primary amenorrhea. Those cases were diagnosed as Turner syndrome (TS), Mayer Rokitansky Küster Hauser syndrome (MRKH) and hipogonadotropic hipogonadism (HH) thanks to the methods we have mentioned above.

Anahtar Kelimeler

• Amenorrhea,Turner Syndrome,Young Adult,Female,Hypogonadism

Kaynakça

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