Idiopathic calcinosis cutis of the vulva in an adult woman, a case report

Abstract

Calcinosis cutis is an uncommon entity defined as the deposition of amorphous calcium and phosphate salts under epidermis. Idiopathic calcinosis cutis occurs in the absence of any metabolic disorder or tissue damage. A 40-year-old multiparous female presented with vulvar nodular masses with discomfort during intercourse only. Physical examination revealed a yellowish colored non-tender, pedunculated nodules measuring approximately 3×1 cm in the left side of vulva. The mass localized between labia minora and labia majora was solid, surfaced with the white pigmentation, irregular, fixed and in sessile nature. Laboratory evaluation revealed normal serum calcium and phosphorus levels and all other laboratory values were within normal reference ranges. Total surgical excision of the mass was performed under general anesthesia. The histopathological diagnosis revealed a calcinosis cutis of the vulva and no recurrence was detected 12 months after the initial treatment. 

Keywords

• Skin neoplasms
• calcinosis
• vulvar dise- ases

Yetişkin bir hastada idiyopatik vulvar kalsinozis, olgu sunumu

Öz

Kalsinozis kutis epidermis altına çözünemeyen kalsiyum fosfat tuzlarının birikmesi ile oluşan nadir bir hastalıktır. İdiopatik form metabolik hastalık veya doku hasarı olmadan ortaya çıkar. Tek şikâyeti ilişki sırasında rahatsızlık hissi olan, 40 yaşında multipar hasta vulvar kitle şikâyeti ile başvurdu. Muayenede sol vulvar bölgede sarımsı renkte, ağrısız, yaklaşık 3x1 cm boyutlarında nodüler lezyon gözlendi. Kitle labium minör ile labium majus arasında lokalize, üzerinde yer yer beyaz pigmentasyon olan, irregüler sınırlı, sert, fikse ve sapsız vasıftaydı. Hastanın serum kalsiyum fosfat düzeyleri ve diğer bütün laboratuar testleri normal referans aralığındaydı.  Genel anestezi altında lezyon total eksize edildi. Histopatolojik inceleme sonucu vulvar kalsinozis kutis olarak gelen hastanın daha sonraki 12 aylık takiplerinde rekürrens gözlenmedi. 

Anahtar Kelimeler

• Deri neoplazmları
• kalsinoz
• vulvar hastalıklar

Kaynakça

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